Bladder duplication

  • 文章类型: Case Reports
    膀胱重复(BD)是一种罕见的畸形,通常与其他异常有关。我们报告一名新生儿在矢状面被诊断为BD,与持续性泌尿生殖窦(UGS)相关,考虑到膀胱颈正下方的阴道开口。这是该协会第四次报告。进行了手术修复:两个膀胱都连接在一起,将共同通道保留为尿道,并通过带有肠段的阴道成形术使阴道下降。她还出现了前肛门,需要后路动员。患者目前3岁,括约肌控制良好。
    Bladder duplication (BD) is a rare malformation that is often associated to other anomalies. We report a newborn diagnosed with BD in the sagittal plane, associated to persistent urogenital sinus (UGS), given the opening of the vagina immediately below the bladder neck. It is the fourth time this association is reported. Surgical repair was made: both bladders were joined, the common channel was left as urethra and the vagina was descended with a vaginoplasty with an intestinal segment. She also presented an anterior anus, that required posterior mobilization. The patient is currently 3 years old with good sphincter control.
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  • 文章类型: Case Reports
    背景:膀胱-外翻-外翻综合征(BEEC)包含广泛的先天性畸形。一名天真的难民被称为我们的中心,被称为BEEC。
    方法:一名27岁女性患者因出生后完全失禁而被难民中心的全科医生转诊。确定了一个带有盲端输尿管口的异型膀胱和第二个带有两个原位输尿管的非异型膀胱,在矢状面显示膀胱重复。进行了剖腹手术,尾端解剖外生膀胱板,并将其用作腹侧包以扩大非外生膀胱。在膀胱颈周围使用自体筋膜吊带进行Mitchell型膀胱颈重建,以获得节制。由于病人从未自愿作废,手术后自发排尿的几率很低.因此,还实现了大陆Mitrofanoff型膀胱造口术的创建,并实现了生殖器重建。
    结果:术后12个月,病人完全是大陆,膀胱容量为250毫升,每天进行5次自我导尿。术后无并发症发生。
    结论:接纳政治难民可能涉及成人先天性畸形的挑战性手术,比如BEEC。这表明了多学科过渡护理的重要性。
    The bladder-Exstrophy-Epispadias complex (BEEC) contains a wide spectrum of congenital malformations. A treatment naïve refugee was referred to our center with what was identified as BEEC.
    A 27-year-old female patient was referred for total incontinence since birth by the general practitioner from the refugee center. An exstrophic bladder with blind ending ureteral orifices and a second non-exstrophic bladder with two orthotopic ureters was identified, demonstrating the bladder duplication in the sagittal plane. Laparotomy was performed, dissecting the exstrophic bladder plate caudally and using it as a ventral onlay to augment the non-exstrophic bladder. A Mitchell-type bladder neck reconstruction was performed with an autologous fascia sling around the bladder neck to obtain continence. As the patient had never voluntarily voided, chances of spontaneous voiding after surgery were low. Therefore creation of a continent Mitrofanoff-type vesicostomy was additionally realized and genital reconstruction was achieved.
    12 months post operatively, the patient was completely continent, had a bladder capacity of 250 ml, and performed self-catheterization 5 times a day. No post-operative complications were observed.
    Admission of political refugees can implicate challenging surgeries for congenital malformations in adults, such as BEEC. This demonstrates the importance of multidisciplinary transitional care.
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  • 文章类型: Case Reports
    Complete diphallia, a rare urogenital congenital anomaly in which a male is born with two fully formed phalluses, occurs in one out of every five to six million live births. The condition is characterized by two separate phalluses, each of which comprise a pair of corpora cavernosa and one corpus spongiosum with an orthotopic urethra. Approximately 100 cases have been reported worldwide, and it is thought that each case is unique. This article discusses diphallia, urethral duplication, and bladder duplication and concludes with a case study involving a three-year-old male born to consanguineous parents from a small, remote community in Ecuador who underwent surgery for correction of a complete coronal penile and bladder duplication. After consultation, the patient was scheduled for a right penectomy and cystoplasty.
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  • 文章类型: Case Reports
    Anorectal malformations are a common congenital anomaly, while bladder duplication is rare. Bladder duplications are classified as complete or incomplete and sagittal or coronal. We present a rare case of coronal complete bladder duplication with rectoprostatic fistula to the blind ending prostatic urethra of the duplicated bladder.
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