关键词: Anorectal malformation Bladder duplication Case report Persistent urogenital sinus

来  源:   DOI:10.1016/j.eucr.2024.102736   PDF(Pubmed)

Abstract:
Bladder duplication (BD) is a rare malformation that is often associated to other anomalies. We report a newborn diagnosed with BD in the sagittal plane, associated to persistent urogenital sinus (UGS), given the opening of the vagina immediately below the bladder neck. It is the fourth time this association is reported. Surgical repair was made: both bladders were joined, the common channel was left as urethra and the vagina was descended with a vaginoplasty with an intestinal segment. She also presented an anterior anus, that required posterior mobilization. The patient is currently 3 years old with good sphincter control.
摘要:
膀胱重复(BD)是一种罕见的畸形,通常与其他异常有关。我们报告一名新生儿在矢状面被诊断为BD,与持续性泌尿生殖窦(UGS)相关,考虑到膀胱颈正下方的阴道开口。这是该协会第四次报告。进行了手术修复:两个膀胱都连接在一起,将共同通道保留为尿道,并通过带有肠段的阴道成形术使阴道下降。她还出现了前肛门,需要后路动员。患者目前3岁,括约肌控制良好。
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