Bladder duplication

  • 文章类型: Case Reports
    背景:膀胱-外翻-外翻综合征(BEEC)包含广泛的先天性畸形。一名天真的难民被称为我们的中心,被称为BEEC。
    方法:一名27岁女性患者因出生后完全失禁而被难民中心的全科医生转诊。确定了一个带有盲端输尿管口的异型膀胱和第二个带有两个原位输尿管的非异型膀胱,在矢状面显示膀胱重复。进行了剖腹手术,尾端解剖外生膀胱板,并将其用作腹侧包以扩大非外生膀胱。在膀胱颈周围使用自体筋膜吊带进行Mitchell型膀胱颈重建,以获得节制。由于病人从未自愿作废,手术后自发排尿的几率很低.因此,还实现了大陆Mitrofanoff型膀胱造口术的创建,并实现了生殖器重建。
    结果:术后12个月,病人完全是大陆,膀胱容量为250毫升,每天进行5次自我导尿。术后无并发症发生。
    结论:接纳政治难民可能涉及成人先天性畸形的挑战性手术,比如BEEC。这表明了多学科过渡护理的重要性。
    The bladder-Exstrophy-Epispadias complex (BEEC) contains a wide spectrum of congenital malformations. A treatment naïve refugee was referred to our center with what was identified as BEEC.
    A 27-year-old female patient was referred for total incontinence since birth by the general practitioner from the refugee center. An exstrophic bladder with blind ending ureteral orifices and a second non-exstrophic bladder with two orthotopic ureters was identified, demonstrating the bladder duplication in the sagittal plane. Laparotomy was performed, dissecting the exstrophic bladder plate caudally and using it as a ventral onlay to augment the non-exstrophic bladder. A Mitchell-type bladder neck reconstruction was performed with an autologous fascia sling around the bladder neck to obtain continence. As the patient had never voluntarily voided, chances of spontaneous voiding after surgery were low. Therefore creation of a continent Mitrofanoff-type vesicostomy was additionally realized and genital reconstruction was achieved.
    12 months post operatively, the patient was completely continent, had a bladder capacity of 250 ml, and performed self-catheterization 5 times a day. No post-operative complications were observed.
    Admission of political refugees can implicate challenging surgeries for congenital malformations in adults, such as BEEC. This demonstrates the importance of multidisciplinary transitional care.
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  • 文章类型: Case Reports
    膀胱重复是一种极为罕见的泌尿系统先天性异常,在男孩中更为常见;文献仅限于病例报告和病例系列。我们描述了两名女婴的膀胱重复畸形病例,其中不包括Abrahamson分类中的完全矢状间隔的罕见变异。诊断采用磁共振尿路造影,结合优秀的解剖信息和尿道的静态和动态评估。手术探查证实了MR尿路造影提供的诊断信息。这些病例为儿科放射科医师和泌尿科医师提供了机会,以了解更多有关膀胱重复的信息,并改善他们对这种罕见疾病的诊断。
    Bladder duplication is an extremely rare congenital anomaly of the urinary system that is more frequent in boys; the literature is limited to case reports and case series. We describe two cases of bladder duplication in two infant girls with an uncommon variant of complete sagittal septum not included in the Abrahamson classification. The diagnosis was made using magnetic resonance urography, combining excellent anatomical information and static and dynamic evaluation of the urinary tract. The diagnostic information provided by MR-urography was confirmed on surgical exploration. These cases provide an opportunity for paediatric radiologists and urologists to learn more about bladder duplication and improve their diagnosis of this rare condition.
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  • 文章类型: Case Reports
    Bladder duplication is an extremely rare congenital urinary tract malformation that is often discovered incidentally. Here, we report a case of incomplete bladder duplication diagnosed by SPECT/CT in a 65-y-old man with lung cancer. Compared with the results of whole-body planar bone scintigraphy, this SPECT/CT finding caused the diagnosis to be revised in this patient with suspected bone metastases. To our knowledge, this is the first documented case of incomplete bladder duplication discovered by SPECT/CT.
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  • 文章类型: Case Reports
    Complete diphallia, a rare urogenital congenital anomaly in which a male is born with two fully formed phalluses, occurs in one out of every five to six million live births. The condition is characterized by two separate phalluses, each of which comprise a pair of corpora cavernosa and one corpus spongiosum with an orthotopic urethra. Approximately 100 cases have been reported worldwide, and it is thought that each case is unique. This article discusses diphallia, urethral duplication, and bladder duplication and concludes with a case study involving a three-year-old male born to consanguineous parents from a small, remote community in Ecuador who underwent surgery for correction of a complete coronal penile and bladder duplication. After consultation, the patient was scheduled for a right penectomy and cystoplasty.
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  • 文章类型: Case Reports
    Complete bladder duplication is a male predominant rare congenital malformation usually diagnosed at birth. Owing to the rarity of this anomaly, only few reports have discussed the surgical approach for this condition, with the open approach for excision being the most common. We hereby present a video of a laparoscopic resection of complete bladder and urethral duplication in a 1-year-old male.
    The patient presented to our clinic with a red mucosal tissue protruding from a cutaneous opening at the dorsal base of the penis that has been present from birth. A normally located and functioning bladder and urethra were present. During work-up, a cystic mass located above the bladder was discovered in imaging examinations. No other anomalies were found. After a shared decision process, we performed a laparoscopic transperitoneal bladder duplication excision during which the accessory urethra and duplicated bladder were removed with preservation of the adjacent normal urethra. The patient had an uneventful recovery with excellent cosmetic results.
    The minimally invasive approach can be utilized for treatment of complex urinary anomalies in young children.
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  • 文章类型: Case Reports
    Anorectal malformations are a common congenital anomaly, while bladder duplication is rare. Bladder duplications are classified as complete or incomplete and sagittal or coronal. We present a rare case of coronal complete bladder duplication with rectoprostatic fistula to the blind ending prostatic urethra of the duplicated bladder.
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