Regional odontodysplasia is a rare developmental disorder characterised by hypoplasia and hypomineralisation of enamel and dentin. Our systematic review aimed to organise the knowledge on localisation, symptomatology and treatment methods in patients with regional odontodysplasia based on case reports published in the databases PubMed, Scopus and Web of Science. Case reports were described in 28 different countries, considering 180 patients (including 91 females). Regional odontodysplasia occurs mainly in both deciduous and permanent dentition (66.1%). The affected teeth were observed more frequently in the maxilla (70.0%), especially on the left side (45.6%). The most common reported symptoms were ghost teeth, poorly developed buds, yellowish-brown colour of crowns and delayed eruption of permanent teeth in affected quadrants. The most popular treatment method was surgical treatment (78.6%) with subsequent prosthetic therapy (34.6%). Based on the review of cases, pathognomonic clinical and radiological signs can be found, however, it is difficult to reach a consensus on the choice of treatment method.

The aim of this article was to review the literature and present a case of regional odontodysplasia (ROD) with special emphasis on clinical and radiographic features. A 6-year-old girl was referred to our department with the chief complaint of missing her permanent maxillary left central incisor, lateral incisor, and both of her canines. The gingiva of the involved region was enlarged, fibrous, and tense. Radiographic examination showed abnormal tooth formation and shortened roots. After 3 years of follow up with temporary prosthetic rehabilitation, periodontal surgery was performed. Following forced eruption and levelling, abnormal tooth eruption and root development were observed. ProRoot MTA (Dentsply-Maillefer, Ballaigues, Switzerland) was used for root canal treatment. Intracanal fiber posts selected and access cavities were restored with composite resin. Prosthetic rehabilitation was completed with zirconia ceramic crowns. The time of diagnosis, characteristics of the present/existing symptoms, and functional and esthetic needs of the patient should be considered to determine the optimal treatment modality for ROD.
Bu makalenin amacı bir rejyonel odontodisplazi (ROD) olgusunun klinik ve radyografik özelliklerini sunmak ve bu konu ile ilgili güncel kaynakları derlemektir. 6 yaşındaki kız hasta üst çene sürekli orta kesici, yan kesici ve kanin dişilerindeki sürme problemleri ve bu dişlerin eksikliği şikayetleri ile kliniğimize başvurmuştur. Klinik muayenede etkilenen bölgede dişetinin büyümüş, fibröz ve gergin olduğu izlenmiştir. Radyografik muayenede kısa köklü anormal şekilli dişler izlenmiştir. Hasta geçici protez ile 3 yıl takip edildikten sonra periodontal cerrahi uygulanmıştır. Dişlerin sürdürülmesi ve ortodontik olarak sıralanmasını takiben anormal diş sürmesi ve anormal kök gelişimi izlenmiştir. ProRoot MTA (Dentsply-Maillefer, Ballaigues, Switzerland) materyali ile kök kanal tedavisi sonrası fiber post seçilmiş ve zirkonyum seramik kuronlar uygulanmıştır. ROD olgularında en uygun tedavi yaklaşımını seçmek için tanı zamanı, mevcut belirtiler ve hastanın işlevsel ya da estetik gereksinimleri değerlendirilmelidir.

Regional odontodysplasia (RO) also known as ghost teeth is a rare developmental anomaly affecting the mesodermal and ectodermal components of teeth with characteristic clinical and radiographic findings. The enamel and dentin are hypomineralized and hypocalcified with short roots and open apices. The affected teeth have an abnormal morphology, meaning they are fragile and thin and liable to fracture and decay. Radiographically, there is a marked reduction in radiodensity with little distinction between the enamel and dentin, hence the term \"ghost teeth.\" RO generally affects one particular segment in one or both arches of the maxilla or mandible and can affect both the primary and permanent dentition. We report a unique case of a 3-year-old female who presented to Alder Hey Children\'s Hospital acutely unwell with a left-sided cervicofacial swelling from RO affecting the entire portion of the left maxilla.