Abstract：
Regional odontodysplasia is a rare developmental disorder characterised by hypoplasia and hypomineralisation of enamel and dentin. Our systematic review aimed to organise the knowledge on localisation, symptomatology and treatment methods in patients with regional odontodysplasia based on case reports published in the databases PubMed, Scopus and Web of Science. Case reports were described in 28 different countries, considering 180 patients (including 91 females). Regional odontodysplasia occurs mainly in both deciduous and permanent dentition (66.1%). The affected teeth were observed more frequently in the maxilla (70.0%), especially on the left side (45.6%). The most common reported symptoms were ghost teeth, poorly developed buds, yellowish-brown colour of crowns and delayed eruption of permanent teeth in affected quadrants. The most popular treatment method was surgical treatment (78.6%) with subsequent prosthetic therapy (34.6%). Based on the review of cases, pathognomonic clinical and radiological signs can be found, however, it is difficult to reach a consensus on the choice of treatment method.
摘要：
区域性牙齿发育不良是一种罕见的发育障碍，其特征是牙釉质和牙本质的发育不全和矿化不足。我们的系统综述旨在组织本地化知识，根据PubMed数据库中发布的病例报告，对区域性牙齿发育不良患者的症状学和治疗方法，Scopus和WebofScience病例报告在28个不同的国家进行了描述，考虑180名患者（包括91名女性）。区域性牙列发育不良主要发生在乳牙和恒牙中（66.1％）。受影响的牙齿在上颌骨中观察到更频繁（70.0％），尤其是左侧（45.6%）。最常见的症状是鬼牙，发育不良的芽，牙冠的黄棕色和受影响象限的恒牙的延迟萌出。最流行的治疗方法是手术治疗（78.6％）和随后的假体治疗（34.6％）。根据对案件的审查，可以发现病理临床和放射学体征，然而,治疗方法的选择很难达成共识。
