背景:软骨粘液样纤维瘤(CMF)是一种罕见的良性骨肿瘤,通常会影响长骨,只有2%的CMF涉及面部骨骼或头骨,到目前为止,zy骨定位极为罕见,只有8例文献报道。
方法:我们报告了一例88岁患者,在1年左右出现右侧颧骨疼痛性肿胀,数量逐渐增加,计算机断层扫描(CT)扫描显示右zh骨的溶骨性病变,皮质破坏。手术治疗包括使用口腔内方法刮骨术,组织病理学结果有利于CMF的诊断.
结论:CF是一种罕见的骨肿瘤,占所有骨肿瘤的不到1%,颌面部骨骼很少受到影响,以下颌骨为好发部位,颧骨位置极为罕见。临床表现不典型,放射学,病变通常为溶骨性,边缘清晰。整块切除是黄金标准,一些作者建议采取保守的方法来避免审美和功能后遗症。
结论:我们报道了一种非常罕见的CF表现,涉及通过保守方法治疗的zy骨。
BACKGROUND: Chondromyxoid fibroma (CMF) is a rare benign bone tumor that typically affects long bones, only 2% of CMFs involved facial bones or skull, zygomatic localization is extremely rare with only 8 cases reported in literature so far.
METHODS: We report a case of 88 old years patient with painful swelling in the right zygomatic around 1 year, progressively increasing in volume, Computed tomography (CT) scan showed an osteolytic lesion in the right zygomatic bone with cortical destruction. Surgical management consisted of bone curettage using intra oral approach, the histopahological findings were in favor of the diagnosis of CMF.
CONCLUSIONS: CF is a rare bone tumor and represents less than 1% of all bone tumors, the maxillofacial bones are rarely affected, with the mandible as a site of predilection, the zygomatic location is extremely rare. The clinical presentation is not typical, radiologically, the lesion is usually osteolytic with well defined margins.En bloc resection is the gold standard, some authors recommand conservative approach to avoid esthetic and functional sequels.
CONCLUSIONS: We reported a very rare presentation of CF involving zygomatic bone treated by conservative approach.