Bochdalek hernia

Bochdalek 疝气
  • 文章类型: Case Reports
    隔膜的先天性缺陷,被称为Bochdalek疝气(BH),是一种允许腹部内脏突出进入胸部的疾病。BH是最常见的先天性膈疝(CDH)类型,通常在左侧检测到。异位肾脏是一种罕见的疾病。胸内异位肾脏是一种极其罕见的疾病。在成年患者中,胸内肾BH的存在极为罕见,通常是无意发现的。一名51岁的男性患者被送往肺科门诊。他表示自己一直有咳嗽等症状,喘息,呼吸困难一年。胸部X射线检查显示左下区域有明确的不透射线的病变。胸部计算机断层扫描(CT)扫描显示左半膈后外侧区域有缺陷,以及左肾突出和左半胸腹膜后脂肪。发现胸内异位肾大小正常,表现为正常衰减和增强,在CT尿路造影期间,造影剂迅速排泄到骨盆系统中。由于疝气体积小,CT尿路造影缺乏异常,患者被建议保守治疗.每年对患者进行随访检查。在整个随访期间,没有一例肾脏相关问题.为了避免不必要的图像引导活检和外科手术,对于出现胸部肿块或半膈肌抬高的患者,必须寻找胸内肾脏。
    A congenital defect in the diaphragm, known as a Bochdalek hernia (BH), is a condition that allows herniation of the abdominal viscera into the thorax. BH is the most common type of congenital diaphragmatic hernia (CDH) and is typically detected on the left side. An ectopic kidney is a rare condition. An intra-thoracic ectopic kidney is an extremely uncommon condition. In adult patients, the presence of BH with an intra-thoracic kidney is extremely uncommon and is often a finding discovered unintentionally. A 51-year-old male patient presented to the outpatient unit of the pulmonology department. He stated that he had been suffering symptoms such as coughing, wheezing, and breathing difficulties for one year. A chest X-ray showed a well-defined radio-opaque lesion in the lower left zone. A computed tomography (CT) scan of the chest demonstrated a defect in the posterolateral region of the left hemidiaphragm, as well as herniation of the left kidney and retroperitoneal fat in the left hemithorax. The intra-thoracic ectopic kidney was found to be normal in size and showed normal attenuation and enhancement, with the contrast being promptly excreted into the pelvicalyceal system during CT urography. Due to the hernia\'s small size and lack of abnormalities on CT urography, the patient was recommended a conservative treatment. A follow-up examination was performed on the patient annually. Throughout the follow-up period, there was not a single episode of kidney-related issues. To avoid unwanted image-guided biopsies and surgical procedures, it is imperative to look for intra-thoracic kidneys in patients presenting with a thoracic mass or an elevated hemi-diaphragm.
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  • 文章类型: Case Reports
    右侧后膈疝是一种罕见的诊断,尤其是在成人人群中。该患者在调查前出现右胸痛20年。在这种情况下,成像提供了准确的诊断。可以通过腹腔镜安全地进行修复。
    Right sided posterior diaphragmatic hernias are a rare diagnosis, especially in adult populations. This patient presented with right thoracic pain for 20 years before investigation. Imaging has provided an accurate diagnosis in this case. Repair can be done safely laparoscopically.
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  • 文章类型: Case Reports
    Bochdalek疝气是the肌的遗传性后外侧缺损,可使腹部器官疝入胸腔。除了是最常见的先天性膈疝(CDH),它也是大多数时间在左半胸部观察到的类型。异位肾是一种罕见的疾病,而异位胸内肾的发生更是少见,仅占所有肾脏异位病例的少数。与Bochdalek疝气相关的胸内肾的发生在成年人中很少见,通常是偶然发现。一名52岁的肥胖女性患者出现在肺科门诊病房,并报告出现咳嗽症状,喘息,三年来呼吸困难.胸部X光片显示右侧隔膜的圆顶升高。胸部计算机断层扫描(CT)显示右半隔膜后部有缺陷,右肾突出,腹膜后脂肪进入右半胸部。CT尿路造影显示胸内肾脏大小正常,增强,造影剂迅速排泄到骨盆系统中。关于疝的小尺寸,并考虑到CT尿路造影没有并发症,建议对患者进行保守治疗。每年对患者进行随访。随访期间无肾脏并发症发生。在评估患有“半膈肌抬高”或“胸部肿块”的患者时,必须检查胸内肾的存在,以避免不良的外科手术和图像引导活检.
    Bochdalek hernia is an inherited posterior lateral defect in the diaphragm that allows the abdominal organs to herniate into the thoracic cavity. In addition to being the most prevalent variety of congenital diaphragmatic hernia (CDH), it is also the type that is observed on the left hemithorax the majority of the time. Ectopic kidney is an uncommon condition, and the occurrence of ectopic intrathoracic kidney is even more uncommon, accounting for only a few of all the cases of renal ectopias. The occurrence of intrathoracic kidney associated with Bochdalek hernia is infrequent among adult individuals and is typically an incidental finding. A 52-year-old obese female patient presented to the pulmonology outpatient unit and reported experiencing the symptoms of coughing, wheezing, and difficulty in breathing since three years. A chest radiograph revealed an elevated dome of the diaphragm on the right side. A computed tomography (CT) of the chest revealed a defect in the posterior aspect of the right hemi-diaphragm with herniation of the right kidney and retroperitoneal fat into the right hemi-thorax. CT urography showed normal size and enhancement of the intrathoracic kidney with prompt excretion of contrast into the pelvicalyceal system. With regard to the small size of the hernia and considering the absence of complications on CT urography, a conservative treatment was proposed to the patient. The patient was followed up every year. There was no occurrence of renal complications during the follow-up period. When evaluating patients with \'elevated hemi-diaphragm\' or thoracic \'mass\', it is essential to check for the presence of intrathoracic kidney to avoid undesirable surgical procedures and image-guided biopsies.
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  • 文章类型: Case Reports
    背景:Bochdalek疝(BH)是一种先天性膈疝,通常在新生儿期发展。BH通常发生在隔膜的左侧。成人的右侧BH很少见。
    方法:一名45岁的男子因体检时胸部X线照片上的异常阴影而被转诊到我们医院。胸部X光片显示右半膈抬高。计算机断层扫描显示多个腹内器官脱垂到右胸腔,对应于右侧BH。突出的内容物包括胃,横结肠,还有肝脏的左叶.肝脏左叶肿大,特别是中间段。进行腹腔镜手术。然而,肝脏的左叶完全被困在胸腔中。因此,必须进行胸腔镜操作才能将肝脏返回腹腔。疝用间断的不可吸收缝线修复,并用网片加固。
    结论:腹腔镜和胸腔镜联合手术成功治疗右侧BH并肝大量脱垂和肝脏形态异常。
    BACKGROUND: A Bochdalek hernia (BH) is a congenital diaphragmatic hernia that often develops in the neonatal period. BH typically occurs on the left side of the diaphragm. A right-sided BH in an adult is rare.
    METHODS: A 45-year-old man was referred to our hospital because of an abnormal shadow seen on chest radiography during a medical check-up. A chest radiograph showed elevation of the right hemidiaphragm. Computed tomography showed prolapse of multiple intraabdominal organs into the right thoracic cavity, corresponding to a right-sided BH. The herniated contents included the stomach, transverse colon, and left lobe of the liver. The left lobe of the liver was enlarged, particularly the medial segment. Laparoscopic surgery was performed. However, the left lobe of the liver was completely trapped in the thoracic cavity. Therefore, thoracoscopic manipulation had to be performed to return the liver to the abdominal cavity. The hernia was repaired with interrupted nonabsorbable sutures and reinforced with mesh.
    CONCLUSIONS: Combined laparoscopic and thoracoscopic surgery was successfully performed for right-sided BH with massive liver prolapse and abnormal liver morphology.
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  • 文章类型: Case Reports
    Bochdalek疝气是一种罕见的先天性膈疝,通常在婴儿期被诊断为左侧。我们报告了一例78岁的女性,该女性患有右侧后外侧膈疝,其中包含多个肠环,有缺血迹象以及4型食管旁疝。胃在有机轴平面上旋转,十二指肠位于纵隔内.患者被紧急采取剖腹探查术。发现并切除了包含50厘米绞窄小肠的后外侧疝缺损,进行了原发性吻合器肠肠造口术,并首先修复了疝缺损。胃减少了,进行了一次crura修复,用胃空肠造口管进行胃切除术。病人被转移到重症监护室,随后拔管,开始肠内喂养,并预计将出院到熟练的护理机构。此病例突显了成人先天性膈疝的罕见无创伤表现。由于其右侧偏侧和绞窄的小肠,其稀有性进一步表示为通常的腹部突出器官是肝脏或结肠。
    A Bochdalek hernia is a rare congenital diaphragmatic hernia often diagnosed in infancy and classically occurring on the left side. We report a case of a 78-year-old female who presented with a right-sided posterolateral diaphragmatic hernia containing multiple loops of bowel with evidence of ischemia as well as a type 4 paraesophageal hernia. The stomach was rotated on the organoaxial plane, and the duodenum was within the mediastinum. The patient was taken emergently for an exploratory laparotomy. A posterolateral hernia defect containing 50 cm of strangulated small bowel was identified and resected, a primary stapled enteroenterostomy was performed and the hernia defect was repaired primarily. The stomach was reduced, a primary crura repair was performed, and gastropexy was performed with a gastrojejunostomy tube. The patient was transferred to the intensive care unit, and subsequently extubated, enteral feeds were initiated, and had anticipated discharge to a skilled nursing facility. This case highlights an uncommon atraumatic presentation of an adult with a congenital diaphragmatic hernia. Its rarity is further denoted due to its right-sided laterality and strangulated small bowel as the usual herniated abdominal organs are the liver or colon.
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  • 文章类型: Journal Article
    先天性膈疝(CDH)是一种罕见的膈肌发育缺陷,以腹部内容物突出到胸部为特征,导致不同程度的肺发育不全和肺动脉高压。产前诊断和预后因素鉴定的重大进展导致CDH胎儿治疗方法的不断完善。在产后,肺保护性通气的原生质方法,营养,预防感染,早期积极管理肺动脉高压可改善CDH婴儿的结局.CDH的手术修复在大多数情况下并不紧急,可以延迟到患者的肺部状态稳定为止。本文对CDH进行了全面的综述,专注于复杂的病理生理学,产前诊断的进展,胎儿干预,和CDH的最佳产后管理。
    Congenital diaphragmatic hernia (CDH) is a rare developmental defect of the diaphragm, characterized by the herniation of abdominal contents into the chest, resulting in varying degrees of pulmonary hypoplasia and pulmonary hypertension. Significant advances in the prenatal diagnosis and identification of prognostic factors have resulted in the continued refinement of the approach to fetal therapies for CDH. In the postnatal period, protocolized approaches to lung-protective ventilation, nutrition, prevention of infection, and early aggressive management of pulmonary hypertension have led to improved outcomes in infants with CDH. Surgical repair of CDH is not urgent in most circumstances and can be delayed until the pulmonary status of the patient has stabilized. This article provides a comprehensive review of CDH, focusing on the complex pathophysiology, advances in prenatal diagnosis, fetal interventions, and optimal postnatal management of CDH.
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  • 文章类型: Case Reports
    先天性膈疝主要见于婴儿,由于新生儿呼吸窘迫,死亡率很高。最常见的先天性膈疝是Bochdalek疝,发生在后外侧膈肌,左侧是最常见的影响。然而,先天性膈疝在成人中极为罕见,并且由于其微妙的症状而经常被误诊。因此,我们建议,对于所有突发剧烈疼痛或反复出现胸部和腹部模糊症状的患者,应采用CT增强扫描进行早期筛查和诊断.此病例报告显示,成年男性罕见发生Bochdalek疝气。患者进食后出现非特异性腹部症状。疝气导致左肾移位,脾曲的横结肠,大部分胃进入胸腔。这种移位导致左肺肺不张,达到了产能的五分之三。患者使用腹腔镜和开放手术的组合进行了成功的治疗。进行了两周的后续CT扫描,三个月,一年后,病情稳定,没有并发症。
    Congenital diaphragmatic hernias are primarily found in infants and have a high mortality rate due to neonatal respiratory distress. The most common type of congenital diaphragmatic hernia is Bochdalek hernia, which occurs in the posterolateral diaphragm, with the left side being the most commonly affected. However, congenital diaphragmatic hernias are extremely rare in adults and are often misdiagnosed due to their subtle symptoms. Therefore, we suggest that a contrast-enhanced CT scan should be used for early screening and diagnosis in all patients with sudden severe pain or recurrent ambiguous symptoms in the chest and abdomen. This case report presents a rare occurrence of Bochdalek hernia in an adult male. The patient experienced nonspecific abdominal symptoms after eating. The hernia resulted in the displacement of the left kidney, the transverse colon of the splenic flexure, and most of the stomach into the thoracic cavity. This displacement led to atelectasis of the left lung, which reached three-fifths of its capacity. The patient underwent successful treatment using a combination of laparoscopy and open surgery. Follow-up CT scans conducted two weeks, three months, and one year later revealed a stable condition with no complications.
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  • 文章类型: Case Reports
    一名29岁的初产妇在妊娠31周时被转诊为胸内肾(ITK)。超声检查显示左肾胸内放置,肾上腺前位异位。磁共振成像证实膈肌中断和结肠疝。一位女性新生儿,在37周交付,左Bochdalek疝接受了成功的胸腔镜修复。尽管左肺受到压迫,值得注意的是,观察到乐观的肺头比(LHR)值,与有利的结果相关。这个案例突显了ITK的罕见发生,它与Bochdalek疝气有关,以及全面产前评估的重要性。
    A 29-year-old primigravida at 31 weeks of gestation was referred for intrathoracic kidney (ITK). Ultrasound revealed left kidney intrathoracic placement with an anteriorly positioned ectopic adrenal gland. Magnetic resonance imaging confirmed diaphragmatic interruption and colon herniation. A female neonate, delivered at 37 weeks, underwent successful thoracoscopic repair for a left Bochdalek hernia. Despite compression of the left lung, notably optimistic lung-to-head ratio (LHR) values were observed, correlating with favorable outcomes. This case underscores the rare occurrence of ITK, its association with Bochdalek hernia, and the importance of comprehensive prenatal evaluations.
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  • 文章类型: Journal Article
    一种罕见的非食管型跨膈疝,必须与旁食管疝明确区分开来,是以先天性疝-Bochdalek疝和Larey-Morgagni疝的通用名称命名的膈缺损,分别。病因学基础相对简单:预先形成的解剖开口的存在,或不允许从胸部区域转移到腹部区域,或,大多数情况下,反之亦然,从腹部到胸部,各种内脏元素(脾脏,肝脏,胃,结肠,胰腺,等。).除了先天起源,描述了一个比较罕见的群体,约占总数的1-7%:创伤性类型的获得性变体,经常通过冲突型机制,产生膈肌应变/破裂。显然,症状是异质的,取决于疝气的位置,缺陷的尺寸,哪个腹部内脏通过疝开口参与,它的迁移程度,以及是否有容积/缺血/阻塞现象。通常,它的临床表现适中,主要是偶然的发现,大多数是消化表现。严重的消化系统并发症,如绞窄,Volvus,穿孔罕见,并伴有严重休克,在几个非特异性消化前驱体之后突然出现。诊断结合影像学评估(普通放射学,对比,CT)与内窥镜检查。无论膈肌缺损所在的一侧或潜在并发症的继发症状如何,都建议进行手术治疗。方法是胸部的,腹部或胸腹联合入路,经典或微创。大多数情况下,选择方法的类型应考虑两个因素:缺陷的大小,通过CT评估,以及主要并发症的存在。任何大于5cm2(食管裂孔疝表面(HSA))的食管裂孔缺损都有网状加固的正式建议。复发率不容忽视,统计数据表明,术后第一年是复发的主要时期,与缺陷的大小成正比。因此,在需要使用网状物的患者中,复发率介于27%和41%之间(!),而对于初级缝合的病例,即,有适度的膈肌缺陷,这是大约。4%。
    A rare entity of non-hiatal type transdiaphragmatic hernias, which must be clearly differentiated from paraoesophageal hernias, are the phrenic defects that bear the generic name of congenital hernias-Bochdalek hernia and Larey-Morgagni hernia, respectively. The etiological substrate is relatively simple: the presence of preformed anatomical openings, which either do or do not enable transit from the thoracic region to the abdominal region or, most often, vice versa, from the abdomen to the thorax, of various visceral elements (spleen, liver, stomach, colon, pancreas, etc.). Apart from the congenital origin, a somewhat rarer group is described, representing about 1-7% of the total: an acquired variant of the traumatic type, frequently through a contusive type mechanism, which produces diaphragmatic strains/ruptures. Apparently, the symptomatology is heterogeneous, being dependent on the location of the hernia, the dimensions of the defect, which abdominal viscera is involved through the hernial opening, its degree of migration, and whether there are volvulation/ischemia/obstruction phenomena. Often, its clinical appearance is modest, mainly incidental discoveries, the majority being digestive manifestations. Severe digestive complications such as strangulation, volvus, and perforation are rare and are accompanied by severe shock, suddenly appearing after several non-specific digestive prodromes. Diagnosis combines imaging evaluations (plain radiology, contrast, CT) with endoscopic ones. Surgical treatment is recommended regardless of the side on which the diaphragmatic defect is located or the secondary symptoms due to potential complications. The approach options are thoracic, abdominal or combined thoracoabdominal approach, and classic or minimally invasive. Most often, selection of the type of approach should be made taking into account two elements: the size of the defect, assessed by CT, and the presence of major complications. Any hiatal defect that is larger than 5 cm2 (the hiatal hernia surface (HSA)) has a formal recommendation of mesh reinforcement. The recurrence rate is not negligible, and statistical data show that the period of the first postoperative year is prime for recurrence, being directly proportional to the size of the defect. As a result, in patients who were required to use mesh, the recurrence rate is somewhere between 27 and 41% (!), while for cases with primary suture, i.e., with a modest diaphragmatic defect, this is approx. 4%.
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  • 文章类型: Case Reports
    先天性膈疝的Bochdalek疝(BH)在成人中很少见。膈疝的绞合已被认为是严重的并发症。在几个因素中,妊娠是膈疝恶化的重要原因。然而,恶心,呕吐,上腹痛通常被认为是非特异性妊娠相关症状。
    我们报告了一例39岁的病例(GravidaII,第I段)妊娠26+1周时延迟诊断绞窄性内脏疝合并全胃坏疽的多胎女性。术前诊断通过X线检查和磁共振成像(MRI)证实。通过电视辅助胸腔镜检查(VAT)确定疝内容物的大小和严重程度后,我们立即转为剖腹手术.产前皮质类固醇与诊断同时施用以促进胎儿成熟。手术期间母体子宫内的胎儿状况保持良好。在孕妇手术矫正后,应仔细监测胎儿和母亲的临床状况,以实现延迟分娩。在妊娠27+1周时通过剖宫产完成分娩。
    尽管孕妇在怀孕期间罕见的Bochdalek疝,通过多学科护理的早期诊断和适当治疗对于母婴结局至关重要.
    UNASSIGNED: Bochdalek hernia (BH) of congenital diaphragm hernia is infrequently seen in adults. Strangulation of the diaphragm hernia has been recognized as a severe complication. Among several factors, pregnancy is an important cause of diaphragm hernia\'s deterioration. However, nausea, vomiting, and upper abdominal pain are often considered non-specific pregnancy-related symptoms.
    UNASSIGNED: We report a case of a 39-year-old (gravida II, para I) multigravida woman with a delayed diagnosis of strangulated herniated viscera complicating total gastric gangrene at 26+1 weeks\' gestation. The preoperative diagnosis was confirmed by an X-ray examination and magnetic resonance imaging (MRI). After identifying the size and severity of the herniated contents through video-assisted thoracoscopy (VAT), we immediately converted to abdominal laparotomy. Antenatal corticosteroids were administered simultaneously with diagnosis to promote fetal maturity. The fetal condition was maintained well in the maternal uterus during the operation. Careful monitoring of the fetus and the mother\'s clinical conditions should be performed during expectant management to achieve delayed delivery after maternal surgical correction. Delivery was completed through cesarean delivery at 27+1 weeks of gestation.
    UNASSIGNED: Despite the rarity of maternal Bochdalek hernias during pregnancy, early diagnosis and appropriate treatment via multidisciplinary care are essential for maternal and fetal outcomes.
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