关键词: Bochdalek hernia Ectopic adrenal gland Intrathoracic kidney Prenatal diagnosis

Mesh : Humans Female Hernias, Diaphragmatic, Congenital / diagnostic imaging surgery Adult Pregnancy Kidney / diagnostic imaging abnormalities Adrenal Glands / diagnostic imaging Ultrasonography, Prenatal Infant, Newborn Magnetic Resonance Imaging Choristoma / diagnostic imaging surgery diagnosis

来  源:   DOI:10.1007/s00404-024-07449-7   PDF(Pubmed)

Abstract:
A 29-year-old primigravida at 31 weeks of gestation was referred for intrathoracic kidney (ITK). Ultrasound revealed left kidney intrathoracic placement with an anteriorly positioned ectopic adrenal gland. Magnetic resonance imaging confirmed diaphragmatic interruption and colon herniation. A female neonate, delivered at 37 weeks, underwent successful thoracoscopic repair for a left Bochdalek hernia. Despite compression of the left lung, notably optimistic lung-to-head ratio (LHR) values were observed, correlating with favorable outcomes. This case underscores the rare occurrence of ITK, its association with Bochdalek hernia, and the importance of comprehensive prenatal evaluations.
摘要:
一名29岁的初产妇在妊娠31周时被转诊为胸内肾(ITK)。超声检查显示左肾胸内放置,肾上腺前位异位。磁共振成像证实膈肌中断和结肠疝。一位女性新生儿,在37周交付,左Bochdalek疝接受了成功的胸腔镜修复。尽管左肺受到压迫,值得注意的是,观察到乐观的肺头比(LHR)值,与有利的结果相关。这个案例突显了ITK的罕见发生,它与Bochdalek疝气有关,以及全面产前评估的重要性。
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