我们介绍了一例孤立的肝内门体分流,具有主动脉-肝-脐带连接;一名27岁的患者在妊娠27周时被产前诊断为3D多普勒血流。胎儿核型分析正常,对静脉和心血管系统的详细评估显示静脉导管未闭且无其他异常.这些具有孤立肝内分流的胎儿有子宫内生长受限的风险(27%),所有病例的活产儿预后良好.产后随访以控制分流闭合至关重要,因为持续的分流可能导致随后的并发症。
We present a case of isolated intrahepatic portosystemic shunts with an aorto- hepatic-umbilical connection; prenatally diagnosed with 3D Doppler flow in a 27-year-old patient at 27 weeks of gestation. Fetal karyotyping was normal, detailed evaluation of the venous and cardiovascular system showed a patent ductus venosus and no other abnormalities. These fetuses with isolated intrahepatic shunts are at risk for intra-uterine growth restriction (27%), all cases had a good prognosis with live births. Postnatal follow-up to control shunt closure is vital as persistent shunts may lead to subsequent complications.