Prenatal 3D-ultrasound diagnosis of isolated intrahepatic portal-systemic shunt with intact ductus venosus: A case report and literature review.

产前三维超声诊断静脉导管完整的孤立性肝内门静脉分流 1 例并文献复习.

• 发表时间: May 2021
• 来源期刊: Radiol Case Rep
• DOI: 10.1016/j.radcr.2021.02.037
• PMID: 33796163
• 文章类型: Case Reports
• 作者列表: Van Houdt M,van der Merwe J,Gewillig M,De Catte L

关键词: Intrahepatic portosystemic shunt; Prenatal ultrasound; Umbilical-Portal Venous System

Abstract

We present a case of isolated intrahepatic portosystemic shunts with an aorto- hepatic-umbilical connection; prenatally diagnosed with 3D Doppler flow in a 27-year-old patient at 27 weeks of gestation. Fetal karyotyping was normal, detailed evaluation of the venous and cardiovascular system showed a patent ductus venosus and no other abnormalities. These fetuses with isolated intrahepatic shunts are at risk for intra-uterine growth restriction (27%), all cases had a good prognosis with live births. Postnatal follow-up to control shunt closure is vital as persistent shunts may lead to subsequent complications.

摘要

我们介绍了一例孤立的肝内门体分流，具有主动脉-肝-脐带连接；一名27岁的患者在妊娠27周时被产前诊断为3D多普勒血流。胎儿核型分析正常,对静脉和心血管系统的详细评估显示静脉导管未闭且无其他异常.这些具有孤立肝内分流的胎儿有子宫内生长受限的风险（27％），所有病例的活产儿预后良好.产后随访以控制分流闭合至关重要，因为持续的分流可能导致随后的并发症。