Abstract：
Susac syndrome is a rare immune-mediated endotheliopathy affecting the microvasculature. It presents three main symptoms: encephalopathy, branch retinal artery occlusions, and hearing loss . Here we present a new case report focusing on the evolution of the cognitive profile. The patient underwent two neuropsychological examinations. The first, one month after the onset of the symptomatology, highlighted a prevalent involvement of verbal executive functions. The second, conducted six months later, revealed a global improvement in most previously deficient areas, although with the persistence of a difficulty in cognitive estimation. . This case illustrates the importance of a comprehensive analysis of patients with Susac syndrome to appreciate the whole range of cognitive deficits and reliably evaluate symptom evolution.
摘要：
Susac综合征是一种罕见的免疫介导的内皮病，影响微血管系统。它表现出三种主要症状：脑病，视网膜分支动脉阻塞,和听力损失。在这里，我们提出了一个新的病例报告，重点是认知概况的演变。患者接受了两次神经心理学检查。第一,症状发作后一个月，强调了口头执行功能的普遍参与。第二个,六个月后，揭示了以前大多数不足领域的全球改善，尽管在认知估计方面存在困难。.此案例说明了对Susac综合征患者进行全面分析以了解整个认知缺陷并可靠评估症状演变的重要性。
