%0 Case Reports
%T Cognitive profile in a young woman with Susac syndrome: a case report.
%A Basagni B
%A Abbruzzese L
%A Radicchi G
%A Damora A
%A Salti G
%A Malentacchi GM
%A Caputo N
%A Zoccolotti P
%A Scarselli C
%A Mancuso M
%J Neurocase
%V 30
%N 3
%D 2024 Aug 13
%M 38869248
%F 0.781
%R 10.1080/13554794.2024.2366457
%X Susac syndrome is a rare immune-mediated endotheliopathy affecting the microvasculature. It presents three main symptoms: encephalopathy, branch retinal artery occlusions, and hearing loss . Here we present a new case report focusing on the evolution of the cognitive profile. The patient underwent two neuropsychological examinations. The first, one month after the onset of the symptomatology, highlighted a prevalent involvement of verbal executive functions. The second, conducted six months later, revealed a global improvement in most previously deficient areas, although with the persistence of a difficulty in cognitive estimation. . This case illustrates the importance of a comprehensive analysis of patients with Susac syndrome to appreciate the whole range of cognitive deficits and reliably evaluate symptom evolution.