{Reference Type}: Case Reports
{Title}: Cognitive profile in a young woman with Susac syndrome: a case report.
{Author}: Basagni B;Abbruzzese L;Radicchi G;Damora A;Salti G;Malentacchi GM;Caputo N;Zoccolotti P;Scarselli C;Mancuso M;
{Journal}: Neurocase
{Volume}: 30
{Issue}: 3
{Year}: 2024 Aug 13
{Factor}: 0.781
{DOI}: 10.1080/13554794.2024.2366457
{Abstract}: Susac syndrome is a rare immune-mediated endotheliopathy affecting the microvasculature. It presents three main symptoms: encephalopathy, branch retinal artery occlusions, and hearing loss . Here we present a new case report focusing on the evolution of the cognitive profile. The patient underwent two neuropsychological examinations. The first, one month after the onset of the symptomatology, highlighted a prevalent involvement of verbal executive functions. The second, conducted six months later, revealed a global improvement in most previously deficient areas, although with the persistence of a difficulty in cognitive estimation. . This case illustrates the importance of a comprehensive analysis of patients with Susac syndrome to appreciate the whole range of cognitive deficits and reliably evaluate symptom evolution.