Abstract：
Bartter syndrome is a rare disorder characterized by reduced sodium chloride transport in the distal nephrons of the kidney. Its clinical features are renal salt wasting, hypokalemic metabolic alkalosis, elevated renin and aldosterone levels with normal or low blood pressure, polyuria, hypercalciuria and malnutrition. The pathophysiologic and biochemical changes in these patients should be kept in mind when considering anaesthetic management. This case report describes our management in a nineteen months old, 3.6 kg weight male child with Bartter\'s syndrome who underwent elective repair of hiatal hernia and gastrostomy.
摘要：
Bartter综合征是一种罕见的疾病，其特征是肾脏远端肾单位的氯化钠转运减少。它的临床特征是肾盐消耗，低血钾代谢性碱中毒，肾素和醛固酮水平升高与正常或低血压，多尿,高钙尿症和营养不良。在考虑麻醉管理时，应牢记这些患者的病理生理和生化变化。这个案例报告描述了我们在19个月大的时候，3.6公斤体重男性儿童患有Bartter综合征，接受选择性食管裂孔疝修补术和胃造口术。
