原发性肾上腺畸胎瘤是一种罕见病变,误诊率高。鉴于肾上腺畸胎瘤和肾上腺往往是不可分割的,切除受影响的肾上腺似乎是不可避免的。因此,临床医生有必要区分肾上腺畸胎瘤和常见的肾上腺脂肪瘤疾病,比如肾上腺血管平滑肌脂肪瘤,肾上腺髓质脂肪瘤,脂肪瘤,神经节细胞瘤,等等。在这项研究中,我们报告了2007年至2020年在我院接受手术治疗的7例肾上腺成熟畸胎瘤患者的临床和病理特征。我们将文献复习病例的临床特征和手术治疗与我们的病例进行了比较。所有患者均为女性,行开腹肾上腺切除术或腹腔镜肾上腺切除术,分别。在我们的案例中,在最长的13年随访期间没有复发.肾上腺畸胎瘤是罕见且容易忽视的。一旦误诊,外科医生可能需要暂时调整手术,延长手术时间,最终增加手术风险。我们的目标主要是帮助临床医生提高对肾上腺畸胎瘤的认识,提高该病的诊断率,优化治疗决策。
Primary adrenal teratoma is a rare lesion with a high misdiagnosis rate. In view of the fact that adrenal teratoma and adrenal gland are often inseparable, the removal of the affected adrenal gland seems inevitable. Thus, it is necessary for clinicians to differentiate adrenal teratoma from common adrenal lipoma diseases, such as adrenal angiomyolipoma, adrenal myelolipoma, lipoma, gangliocytoma, and so on. In this study, we reported the clinical and pathologic features of 7 patients surgically treated for adrenal mature teratomas from 2007 to 2020 in our hospital. We compared the clinical characteristics and surgical management in literature review cases with our cases. All patients were females and underwent open adrenalectomy or laparoscopic adrenalectomy, respectively. In our cases, there was no recurrence during the longest follow-up of 13 years. Adrenal teratoma is rare and easy to ignore. And once misdiagnosed, the surgeon may need to adjust the operation temporarily, extend the operation time and finally increase the operative risks. Our aim is mainly to help clinicians to raise awareness of adrenal teratomas, improve the diagnosis rates and optimize the treatment decision-making of this disease.