尽管房室间隔缺损是根据解剖房室口分类的,从外科角度来看,心房室间隔缺损的心内分流的位置很重要。在这里,我们报告了三例房室间隔缺损,有一个小的或没有口的原发性缺损。病例1(3个月大的女孩)术前诊断为室间隔缺损,继发孔型房间隔缺损,和二尖瓣裂.手术后,诊断被纠正为房室间隔缺损,并完全修复。病例2(9岁女孩)因室间隔缺损伴跨骑二尖瓣而接受肺动脉束带术。在经历了案例1之后,我们意识到案例1和案例2之间的相似性。因此,我们纠正了房室间隔缺损的诊断并获得了明确的修复.基于这些经验,我们准确诊断病例3(3个月大男孩)患有房室间隔缺损。这种变体鲜为人知;然而,正确的形态学理解对于促进解剖修复和预防术后房室传导阻滞是必要的。这种变异的某些病例可能被诊断为室间隔缺损,二尖瓣跨骑,无法接受明确的修复。裂口的方向,没有房室瓣偏移,和左房室瓣的三叶似乎都对诊断有用,这些可以很容易地通过超声心动图来证实。
Although atrioventricular septal defects are categorized according to the anatomical atrioventricular orifice, the location of the intracardiac shunt in atrioventricular septal defects is important from a surgical perspective. Herein, we report three cases of atrioventricular septal defects with a small or no ostium primum defect. Case 1 (3-month-old girl) was diagnosed preoperatively with a ventricular septal defect, secundum atrial septal defect, and mitral valve cleft. After the operation, the diagnosis was corrected to an atrioventricular septal defect and was repaired completely. Case 2 (9-year-old girl) underwent pulmonary artery banding for a ventricular septal defect with a straddling mitral valve. After the experience with Case 1, we realized similarities between Cases 1 and 2. Therefore, we corrected the diagnosis to atrioventricular septal defect and achieved definitive repair. Based on these experiences, we accurately diagnosed Case 3 (3-month-old boy) with an atrioventricular septal defect. This variant is poorly known; however, proper morphological understanding is necessary to facilitate anatomical repair and prevent postoperative atrioventricular blocks. Some cases of this variant may be diagnosed as a ventricular septal defect with straddling mitral valve and are unable to receive definitive repair. The direction of the cleft, absence of atrioventricular valve offsetting, and trileaflet of the left atrioventricular valve all seem useful for making a diagnosis, and these can be easily confirmed by echocardiography.