患者出现右下肢疼痛性肌肉肿胀,用免疫抑制疗法改善。最初,该病被诊断为多发性肌炎,但不久后复发。成像和活检后,最终诊断为原发性骨骼肌外周T细胞淋巴瘤,未指定(PSM-PTCL,NOS).在这份报告中,我们讨论了诊断和治疗这种侵袭性恶性肿瘤的挑战,并回顾了PSM-PTCL的文献,NOS.要点•迄今为止,关于PSM-PTCL的报道很少,NOS,我们的案子是第十个.•考虑PSM-PTCL至关重要,NOS,当出现局部肌肉水肿和无法解释的疼痛时。•组织病理学检查可能是诊断这种罕见疾病的最有效方法。
The patient presented to the clinic with painful muscle swelling in the right lower extremity, which improved with immunosuppressive therapy. Initially, the condition was diagnosed as polymyositis but recurred soon after. After imaging and biopsy, the final diagnosis was primary skeletal muscle peripheral T-cell lymphoma, not otherwise specified (PSM-PTCL, NOS). In this report, we discuss the challenges in diagnosing and treating this aggressive malignancy and review the literature on PSM-PTCL, NOS. Key Points • To date, there are few reports of PSM-PTCL, NOS, and our case is the tenth. • It is crucial to consider PSM-PTCL, NOS, when presenting with localized muscle edema and unexplained pain. • Histopathological examination is likely the most effective method for diagnosing this rare disease.