背景:自发性眶头颅囊肿是一种罕见的疾病。这项研究的目的是提供一个临床病例的描述,并进行系统的文献综述。
方法:对Pubmed,Scopus,进行了WebofScience数据库,根据PRISMA的建议。
结果:一名6岁患者因右耳乳突炎和乙状结肠和横窦血栓形成而入院,以及颈内静脉的近端部分。放射学检查显示,左眼眶肿块(22×14mm)与无症状的眼眶脑膜膨出(MC)从眶上裂(SOF)突出。这个孩子接受了右乳突切除术。颅内高压(ICH)的症状和体征发展后,进行了血管内血栓切除术和横窦支架置入术,随着临床状况的改善和眼眶MC的减少。系统文献综述涵盖了43例自发性眼眶MC患者的29篇出版物。在大多数情况下,手术是首选治疗方法。
结论:本病例报告和系统评价强调了ICH调查和以病理生理为导向的治疗方法的重要性。文献中描述的经验是有限的,使额外数据的收集变得至关重要。
BACKGROUND: Spontaneous orbital cephaloceles are a rare condition. The purpose of this study is to provide a description of a clinical case and to carry out a systematic literature review.
METHODS: A systematic review of the English literature published on the Pubmed, Scopus, and Web of Science databases was conducted, according to the PRISMA recommendations.
RESULTS: A 6-year-old patient was admitted for right otomastoiditis and thrombosis of the sigmoid and transverse sinuses, as well as the proximal portion of the internal jugular vein. Radiological examinations revealed a left orbital mass (22 × 14 mm) compatible with asymptomatic orbital
meningocele (MC) herniated from the superior orbital fissure (SOF). The child underwent a right mastoidectomy. After the development of symptoms and signs of intracranial hypertension (ICH), endovascular thrombectomy and transverse sinus stenting were performed, with improvement of the clinical conditions and reduction of the orbital MC. The systematic literature review encompassed 29 publications on 43 patients with spontaneous orbital MC. In the majority of cases, surgery was the preferred treatment.
CONCLUSIONS: The present case report and systematic review highlight the importance of ICH investigation and a pathophysiological-oriented treatment approach. The experiences described in the literature are limited, making the collection of additional data paramount.