Dripping candle wax

  • 文章类型: Journal Article
    Melorheostosis是一种非癌性骨病,其特征是骨和软组织生长异常。尽管在近一个世纪前被发现,围绕这种情况还有许多未知的方面。这通常是偶然的发现,患者经历相关的疼痛和畸形。诊断通常依赖于X射线,虽然不是所有的情况下表现出经典的蜡烛蜡的外观。已经提出了一种新的成像标志,称为“盘子上的饺子”,用于MRI和CT扫描的扁平骨骼。在不确定的情况下可能需要活检,因为没有明确的组织学特征。与其他疾病有关的melorheostopsis并不少见,应考虑采用多学科小组的协作方法。在硬化骨疾病的鉴别诊断中应考虑这种情况。管理通常旨在缓解症状,通过保守措施或手术干预。
    Melorheostosis is a noncancerous bone disease characterized by abnormal bone and soft tissue growth. Despite being identified almost a century ago, there are still many unknown aspects surrounding this condition. It can often be an incidental discovery, with patients experiencing associated pain and deformities. Diagnosis typically relies on X-rays, although not all cases exhibit the classic candle wax appearance. A new imaging sign known as the \"dumpling on a plate sign\" has been proposed for flat bones for both MRI and CT scans. A biopsy may be necessary in cases of uncertainty, as there is not a definitive histological feature. It is not uncommon for melorheostosis to be linked with other conditions, and a collaborative approach involving a multidisciplinary team should be considered. This condition should be considered in the differential diagnosis of sclerotic bone conditions. Management is generally aimed at symptom relief, either through conservative measures or surgical intervention.
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  • 文章类型: Case Reports
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  • 文章类型: Case Reports
    Melorheostosis是一种罕见的良性骨病理,涉及骨发育不良和骨增生。该疾病可以通过沿长骨骨干滴落的不透射线病变的特征性影像学特征来识别。异常的骨形成和发育主要表现为疼痛,水肿,和患肢的感觉异常。严重病例可能报告肢体畸形以及活动范围有限。直到现在,全球约有300例报告了有关melorheostosis及其不同的临床表现和年龄分布。在越南,只有一例已知的通过射线照相偶然发现的melorheostosis病例。病例的稀缺在医学界认识和诊断疾病方面提出了挑战,延迟诊断会导致严重挛缩和肢体运动受损。在这篇文章中,我们报道了一例82岁的多发性骨性恶性骨病,迟发性和以水肿为主,影响胸骨,肋骨,和右肢的多个骨骼,并介绍了我们对患有慢性四肢水肿的老年患者的临床方法。我们的病例在解剖位置以及主要的20年非凹陷性水肿方面是独特的。根据经典的滴落蜡烛蜡射线照相特征进行了迅速诊断,强调了普通X射线在建立诊断中的作用,而无需额外利用其他方式和侵入性程序。排除慢性水肿的其他原因,如淋巴结病,恶性肿瘤以及寄生虫感染具有临床意义。
    Melorheostosis is a rare benign bone pathology involving bone dysplasia and hyperostosis. The disease can be recognized with a characteristic radiographic feature of radiopaque lesions dripping along a long bone\'s diaphysis. The aberrant bone formation and development manifests mainly as pain, edema, and paresthesia of the affected limb. Severe cases may report limb deformity as well as limited range of motion. Until now, there have been approximately 300 cases reported about melorheostosis worldwide and its diverse clinical picture and age distribution. In Vietnam, there is only one known case of melorheostosis discovered incidentally via radiography. The scarcity of cases presents a challenge within the medical community in recognizing and diagnosing the condition, and a delayed diagnosis can lead to severe contracture and compromised limb motility. In this article, we reported an 82-year-old case of polyostotic melorheostosis with late onset and predominant edema, affecting the sternum, the ribs, and multiple bones of the right extremities and presented our clinical approach for a geriatric patient with chronic limb edema. Our case is distinctive in terms of anatomical location as well as the predominant 20-year non-pitting edema. A prompt diagnosis was made upon the classic dripping candle wax radiographic features emphasizing the role of plain X-ray in establishing the diagnosis without extraneous utilization of other modalities and invasive procedures. Exclusion of other causes of chronic edema such as lymphadenopathy, malignancy as well as parasitic infection is of clinical importance.
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  • 文章类型: Case Reports
    Melorheostosis is a rare benign bone disease including dysostosis and sclerosis. Dripping candle wax presence is a common and typical sign of melorheostosis. This sign appears as irregular hyperostosis of the cortical bone which is likened to melted wax flowing down one side of a candle. It can sometimes cause pain, stiffness joint, or limitation of motion in the affected areas implicitly but mostly has no symptoms. It is usually observed on plain radiography; its appearance is generally hyperplasia on one side of the bone. We report a 33-year-old male who has an incidental diagnosis of melorheostosis post-trauma.
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  • 文章类型: Journal Article
    重要的是要考虑出现软组织肿胀的患者的罕见情况,关节挛缩,和“滴下的蜡烛蜡”-在手上的X光照片上可见。必须排除临床后遗症,例如腕管综合征或触发手指。对症治疗通常是足够的。
    It is important to consider the rare case of a melorheostosis in patients presenting with soft tissue swelling, joint contractures, and \"dripping candle wax\"-like hyperostoses visible on hand radiographs. Clinical sequelae such as carpal tunnel syndrome or trigger finger have to be ruled out. Symptomatic therapy is usually sufficient.
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