背景:Tessier7裂是罕见的颅面裂痕。活产发生率从1/80,000到1/300,000不等,亚洲人中120个颅面裂的发生率为1。其临床表现的严重程度差异很大,因此,使诊断复杂化,并导致对其手术管理缺乏共识。这项研究的目的是描述临床发现,Tessier裂隙7软组织修复的类型,以及它在吉隆坡医院的结果。
方法:这项回顾性研究回顾了2001年1月至2019年7月手术儿童的记录。有关并发先天性异常的数据,并发症,手术类型,等。,是从门诊记录中收集的,操作注释,和临床照片。
结果:28名儿童接受了治疗,修复了33处(双侧5处)裂痕。男女比例为1.3:1(16名男性和12名女性)。23例患者有单侧裂隙(82.14%),右14(60.86%),左8(34.78%)。双侧裂隙较少见(17.86%)。23例(82.14%)为马来人,3(10.71%)中国人,1名(3.57%)印度人,和1(3.57%)柬埔寨人。11份医疗记录无法追踪(由于不活动的持续时间而中断)。有10次直线维修,5个Z型塑料,并进行了1例W成形术;3例没有详细说明修复类型。一个孩子需要疤痕修复,1例出现肥厚性瘢痕,需要注射皮质类固醇-没有报告进食时言语或口腔功能障碍。随访时间为3至14年。
结论:我们中心的Tessier7裂出勤率较高。直线皮肤修补术结合下朱红色粘膜瓣可用于并发症和翻修手术的低发生率。
Tessier cleft 7 are rare craniofacial clefts. Live-birth incidence varies from 1/80,000 to 1/300,000, with the incidence of 1 in 120 craniofacial clefts among Asians. Its clinical presentation varies widely in severity, thus, complicating diagnosis and contributing to the lack of consensus regarding its surgical management. The aim of this study is to describe clinical findings, types of Tessier cleft 7 soft tissue repair, and its outcomes in Kuala Lumpur Hospital.
This retrospective study reviewed records of children operated from January 2001 to July 2019. Data regarding concurrent congenital anomalies, complications, type of surgery, etc., were collected from outpatient records, operative notes, and clinical photographs.
Twenty-eight children were treated, and 33 clefts (5 bilateral) were repaired. The male-to-female ratio was 1.3:1 (16 males and 12 females). Twenty-three patients had unilateral clefts (82.14%), with 14 right (60.86%) and 8 left (34.78%). Bilateral clefts were less common (17.86%). Twenty-three patients (82.14%) were Malay, 3 (10.71%) Chinese, 1 (3.57%) Indian, and 1 (3.57%) Cambodian. Eleven medical records were untraceable (discontinued due to duration of inactivity). There were 10 straight-line repairs, 5 Z-plasties, and 1 W-plasty performed; 3 cases did not detail the type of repair. One child required scar revision, and 1 had hypertrophic scarring requiring corticosteroid injection-no disturbances in speech or oral incompetency while eating were reported. Duration of follow-up ranged from 3 to 14 years.
Our center has a higher rate of Tessier cleft 7 attendance. Straight-line cutaneous repairs combined with inferior vermilion mucosal flap can be used with low rates of complication and revision surgery.