PDF(Pubmed)
Abstract：
Introduction and importance Tessier 7 craniofacial congenital cleft is a rare anomaly, occurring in about 1 in 80,000 to 1 in 300,000 live births, comprising 0.3% to 1.0% of total cleft cases. A total of 24 cases have been reported since 2000. This case is the 25th instance and possibly the first reported in Nepal.
METHODS: A 3-year-old child, accompanied by parents, presented at the Department of Oral and Maxillofacial Surgery with complaints of feeding difficulties, speech impediment, and aesthetic concerns. Diagnosis revealed Tessier number 7 congenital cleft. Surgical intervention successfully repaired the cleft, involving straight-line closure of mucosa and skin, suturing of perioral muscles to establish a new modiolus and formation of a new commissure. Postoperative follow-up over 6 months demonstrated excellent functional and aesthetic results without any complications.
UNASSIGNED: Tessier 7 congenital cleft arises from anomalous fetal development, stemming from incomplete fusion of the maxillary and mandibular processes of the first pharyngeal arch. Surgical correction poses challenges due to atypical anatomical positioning and cleft appearance. The repair involves layered closure, linear mucosal closure, perioral muscle reorganization to establish a new modiolus, skin closure via straight-line or z-plasty techniques, culminating in the creation of a new commissure.
CONCLUSIONS: Given its rarity, surgeons must be well-versed in the intricate surgical protocol for Tessier 7 cleft treatment. Early intervention is crucial for optimal functional and cosmetic results. Key steps encompass establishing a new modiolus, forming a new commissure, and achieving effective skin closure.
METHODS: A 3-year-old child, accompanied by parents, presented at the Department of Oral and Maxillofacial Surgery with complaints of feeding difficulties, speech impediment, and aesthetic concerns. Diagnosis revealed Tessier number 7 congenital cleft. Surgical intervention successfully repaired the cleft, involving straight-line closure of mucosa and skin, suturing of perioral muscles to establish a new modiolus and formation of a new commissure. Postoperative follow-up over 6 months demonstrated excellent functional and aesthetic results without any complications.
UNASSIGNED: Tessier 7 congenital cleft arises from anomalous fetal development, stemming from incomplete fusion of the maxillary and mandibular processes of the first pharyngeal arch. Surgical correction poses challenges due to atypical anatomical positioning and cleft appearance. The repair involves layered closure, linear mucosal closure, perioral muscle reorganization to establish a new modiolus, skin closure via straight-line or z-plasty techniques, culminating in the creation of a new commissure.
CONCLUSIONS: Given its rarity, surgeons must be well-versed in the intricate surgical protocol for Tessier 7 cleft treatment. Early intervention is crucial for optimal functional and cosmetic results. Key steps encompass establishing a new modiolus, forming a new commissure, and achieving effective skin closure.
摘要：
简介和重要性Tessier7颅面先天性裂是一种罕见的异常，发生在大约8万分之一到30万分之一的活产中，占总裂隙病例的0.3%至1.0%。自2000年以来，共报告了24例病例。这是尼泊尔第25例，也可能是第一例。
方法：一个3岁的孩子，在家长的陪同下,在口腔颌面外科就诊，抱怨进食困难，言语障碍,和美学问题。诊断显示Tessier7号先天性c裂。手术成功修复了裂隙,涉及粘膜和皮肤的直线闭合，缝合口周肌肉以建立新的节状肌并形成新的连合。术后6个月的随访显示出出色的功能和美学效果，无任何并发症。
■Tessier7先天性裂隙源于胎儿发育异常，源于第一咽弓的上颌和下颌突的不完全融合。由于非典型的解剖定位和裂隙外观，手术矫正面临挑战。修复涉及分层闭合，线性粘膜闭合,口周肌肉重组以建立新的modiolus，通过直线或Z-成形术技术闭合皮肤，最终创造了一个新的委员会。
结论：鉴于其稀有性，外科医生必须精通Tessier7裂口治疗的复杂手术方案。早期干预对于最佳功能和美容效果至关重要。关键步骤包括建立新的modiolus，形成一个新的委员会，并实现有效的皮肤闭合。
方法：一个3岁的孩子，在家长的陪同下,在口腔颌面外科就诊，抱怨进食困难，言语障碍,和美学问题。诊断显示Tessier7号先天性c裂。手术成功修复了裂隙,涉及粘膜和皮肤的直线闭合，缝合口周肌肉以建立新的节状肌并形成新的连合。术后6个月的随访显示出出色的功能和美学效果，无任何并发症。
■Tessier7先天性裂隙源于胎儿发育异常，源于第一咽弓的上颌和下颌突的不完全融合。由于非典型的解剖定位和裂隙外观，手术矫正面临挑战。修复涉及分层闭合，线性粘膜闭合,口周肌肉重组以建立新的modiolus，通过直线或Z-成形术技术闭合皮肤，最终创造了一个新的委员会。
结论：鉴于其稀有性，外科医生必须精通Tessier7裂口治疗的复杂手术方案。早期干预对于最佳功能和美容效果至关重要。关键步骤包括建立新的modiolus，形成一个新的委员会，并实现有效的皮肤闭合。
