■纤维瘤病(DF)的特征是罕见的单克隆成纤维细胞增殖,表现出可变且不可预测的临床表现。DF可分为散发性和遗传性。尽管进行了广泛的研究,DF的确切病因仍然难以捉摸。
一名31岁的男性患者出现在医院,右下腹部肿块逐渐增大,伴有腹部不适。入院前1周发现症状。肠镜检查没有发现结肠异常,血液检查没有任何异常。由于手术过程中质量的不确定性,部分切除回肠和盲肠,然后是回肠结肠端对端吻合术,术后无并发症。最终的病理诊断证实远端回肠的原发性纤维样型纤维瘤病(侵袭性纤维瘤病)。为了有效地管理DF,我们建议对患者进行随访.这包括手术后第一年每3个月预约一次,其次是每6个月的任命,直到第五年,此后每年一次.随访检查应包括收集患者的病史,体检,验血,超声波,CT扫描,以及其他相关评估。在后续行动的第一年,没有进行进一步的治疗,患者保持无病。
■起源于小肠的纤维瘤病(DF)是一种极为罕见的疾病,表现出局部侵袭性,可能危及生命。尽管它的组织学是良性的,DF具有高的局部复发率并且缺乏转移潜力。DF的诊断仍然具有挑战性,特别是在由于无症状患者或部分器官受损而导致手术干预不可行的情况下。在这种情况下,建议采用“观察等待”方法作为初始治疗策略。然而,当术前诊断困难时,手术通常被认为是最好的选择。鉴于局部复发的可能性和不确定的长期预后,定期跟进是必要的。
UNASSIGNED: Desmoid-type fibromatosis (DF) is characterized by a rare monoclonal fibroblast proliferation that exhibits variable and unpredictable clinical presentation. DF can be classified into sporadic and hereditary types. Despite extensive research efforts, the exact etiology of DF remains elusive.
UNASSIGNED: A 31-year-old male patient presented to the hospital with a progressively growing mass in the right lower abdomen, accompanied by abdominal discomfort. Symptoms are discovered 1 week before admission. Enteroscopy revealed no evidence of colonic abnormalities, and blood tests did not indicate any abnormalities. Due to the indeterminate nature of the mass during surgery, a partial resection of the ileum and cecum was performed, followed by ileocolonic end-to-end anastomosis, with no postoperative complications. The final pathological diagnosis confirmed primary desmoid-type fibromatosis of the distal ileum (invasive fibromatosis). To effectively manage DF, we recommend a follow-up schedule for patients. This includes appointments every 3 months in the first year following surgery, followed by appointments every 6 months up to the fifth year, and then once a year thereafter. The follow-up examinations should include collection of the patient\'s medical history, physical examination, blood tests, ultrasounds, CT scans, and other relevant assessments. During the first year of the follow-up period, no further treatment was administered, and the patient remained disease-free.
UNASSIGNED: Desmoid-type fibromatosis (DF) originating from the small intestine is an extremely rare condition that exhibits local invasiveness and can be life-threatening. Despite its benign histology, DF has a high local recurrence rate and lacks metastatic potential. Diagnosis of DF remains challenging, especially in cases where surgical intervention is not feasible due to asymptomatic patients or partial organ impairment. In such cases, a \"watchful waiting\" approach is recommended as the initial treatment strategy. However, when preoperative diagnosis is difficult, surgery is typically considered the best option. Given the potential for local recurrence and the uncertain long-term prognosis, regular follow-up is necessary.