该病例报告描述了一名13岁10个月大的女孩,该女孩在12个月大的时候接受了死者供体分裂LT,以初步诊断胆道闭锁。出现下消化道出血的人.超声和CT显示涉及盲肠和升结肠的静脉血管异常,SMV和骨盆静脉的通信与CEPS一致。在沿子宫和膀胱的骨盆中注意到相关的静脉曲张。这些发现通过经肝门静脉造影得到证实,这是诊断和治疗,因为CEPS的成功栓塞是使用微线圈进行的。手术后没有并发症,也没有发生进一步的消化道出血,说明这种治疗方案对CEPS的疗效。我们讨论了关于LT术后胃肠道出血的主诉的文献,CEPS是胃肠道出血的罕见原因及其与PV的关联,以及CEPS的分类和治疗。
This case report describes a 13-year 10-month-old girl who underwent a deceased-donor split LT for primary diagnosis of biliary atresia at the age of 12 months, who presented with a lower GI bleed. Ultrasound and CT revealed a venous vascular anomaly involving the cecum and ascending colon, with communication of the SMV and pelvic veins consistent with a CEPS. Associated varices were noted in the pelvis along the uterus and urinary bladder. These findings were confirmed by trans-hepatic porto-venography, which was diagnostic and therapeutic as a successful embolization of the CEPS was performed using micro-coils. There were no complications following the procedure and no further GI bleeding occurred, illustrating the efficacy of this treatment option for CEPS. We discuss the literature regarding the presenting complaint of GI bleeding post-LT, CEPS as a rare cause of GI bleeding and its association with PV, and the classification and treatment of CEPS.