已经描述了两种主要类型的裂痕手。尺骨裂手部畸形非常罕见，其特征是两个恒定的特征：小指的径向深裂和尺骨指发育不全。尺骨裂隙的发病机制尚不清楚。第二种类型是中央裂手畸形，其特征在于手部中央的软组织/骨缺损。中央裂痕的患者在剩余的手指中也有几个并发畸形。本文回顾了3例尺骨裂手和44例中央裂手的临床特点,特别强调并发畸形。然后提供了作者对两种类型的裂隙及其并发畸形的发病机理的假设。
Two main types of cleft hands have been described. The ulnar cleft hand deformity is very rare and is characterized by two constant features: a deep cleft radial to the little finger and hypoplasia of the ulnar digits. The pathogenesis of ulnar clefts is unknown. The second type is the central cleft hand deformity, which is characterized by a soft tissue/bone defect in the hand centrally. Patients with central clefts also have several concurrent deformities in the remaining digits. This paper reviews the clinical features of three cases with ulnar cleft hands and 44 cases of central cleft hands, with special emphasis on concurrent deformities. The author\'s hypothesis of pathogenesis for both types of clefts and their concurrent deformities is then offered.
