■肾原始神经外胚层肿瘤(rPNET)具有术前诊断困难的特点,高度恶性,易早期转移或术后复发,预后不良,等等。然而,术前无转移的rPNET只有在根治性手术切除后才能有良好的生存预后。
■我们报告一例14岁男性肾肿瘤患者,在手术前或手术后接受了无放疗或化疗的左肾开放根治术,经术后病理结果证实。预后随访,定期复查胸部和整个腹部的CT,血尿分析,肾功能,根据肾癌指南和电解质。
■术后病理证实rPNET,术后未进行辅助放疗或化疗,随访近5年未见肿瘤复发或转移。
■尽管rPNET恶性程度很高,术前无转移的患者通过及时的根治性手术仍可获得良好的生存预后。
UNASSIGNED: Renal primitive neuroectodermal tumor (rPNET) has the characteristics of a difficult preoperative diagnosis, a high degree of malignancy, easy early metastasis or postoperative recurrence, a poor prognosis, and so on. However, rPNET that has no metastasis before surgery can have a good survival prognosis only after radical surgical resection.
UNASSIGNED: We report the
case of a 14-year-old male patient with a renal tumor who underwent open radical left nephrectomy without radiotherapy or chemotherapy before or after surgery, as confirmed by postoperative pathological results. The prognosis was followed up by a regular review of the chest and whole abdomen on CT, hematuria analysis, renal function, and electrolytes according to the guidelines for renal cancer.
UNASSIGNED: Postoperative pathological results confirmed rPNET; no adjuvant radiotherapy or chemotherapy were performed after surgery; no tumor recurrence or metastasis were observed during the follow-up of nearly 5 years.
UNASSIGNED: Despite the high degree of rPNET malignancy, patients without metastases before surgery can still obtain a good survival prognosis through timely radical surgery.