未经证实:婴儿期黑色素神经外胚层肿瘤(MNTI)被普遍描述为一种罕见的,良性,色素性病变,最常累及上颌骨。它的起源已被确定为在神经c细胞中。由于高复发率和模仿恶性肿瘤的攻击行为,这对他们的诊断提出了巨大的挑战,治疗计划,和预后。
UNASSIGNED:两岁的女性没有已知的合并症,主要主诉是上唇区域肿胀。
UNASSIGNED:她在全身麻醉下接受肿瘤切除术。对样本进行组织学和免疫学检查,确认MNTI的诊断。
UNASSIGNED:术后顺利。经过定期随访,患者愈合良好,无复发迹象。
未经评估:根据我们的经验,我们认为MNTI的诊断主要是临床。早期保守性手术切除和定期随访效果良好,预后良好。
UNASSIGNED: Melanotic neuroectodermal tumour of infancy (MNTI) is universally described as a rare, benign, pigmented lesion which most frequently involves the maxilla. Its origin is well established to be in the neural crest cells. Due to the high recurrence rate and aggressive behaviour mimicking malignancy, it poses a great challenge in their diagnosis, treatment planning, and prognosis.
UNASSIGNED: Two-year-old female with no known comorbidities was brought in with the chief complaint of a growing swelling in the upper lip region.
UNASSIGNED: She was taken up for resection of the tumour under general anaesthesia. The specimen was subjected to histological and immunological examination confirming the diagnosis of MNTI.
UNASSIGNED: The postoperative period was uneventful. After regular follow-up, the patient showed satisfactory healing with no signs of recurrence.
UNASSIGNED: Based on our experience, we feel that the diagnosis of MNTI is mainly clinical. Early conservative surgical excision and regular follow-up provide an excellent result with good prognosis.