肝内门静脉络脉是Budd-Chiari综合征(BCS)的特征,通常是小口径的,在多普勒上可见。建立大型门静脉系统分流术,放射学(经颈静脉肝内门体分流术)或手术均可在BCS中获得出色的长期结果。这里,我们报告了三例罕见的无症状BCS,有自发性大型肝内门静脉系统分流。
Intra-hepatic portal-venous collaterals are characteristic of Budd-Chiari syndrome (BCS) and are usually of small caliber and seen on Doppler. Creation of large portal-systemic shunt, either radiologically (Transjugular intrahepatic porto-systemic shunt) or surgically results in excellent long term outcomes in BCS. Here, we report a series of three rare cases of asymptomatic BCS, who had spontaneous large intra-hepatic portal-systemic shunts.