Budd-Chiari Syndrome With Spontaneous Intrahepatic Portosystemic Shunts: A Case Series.

Budd - Chiari 综合征合并自发性肝内门体分流 ： 病例系列。

• 发表时间: May-Jun 2019
• 来源期刊: J Clin Exp Hepatol
• DOI: 10.1016/j.jceh.2018.08.003
• PMID: 31360033
• 文章类型: Journal Article
• 作者列表: Bhatt P,Gupta DK,Agrawal D,Deshmukh H,Rathod K,Shukla A

关键词: BCS, Budd–Chiari Syndrome; HE, Hepatic Encephalopathy; HV, Hepatic Vein; IVC, Inferior Vena Cava; LFT, Liver Function Test; MTHFR, Methylenetetrahydrofolate Reductase; PHT, Portal Hypertension; SIPSS, Spontaneous Intrahepatic Portosystemic venous shunt; TIPSS, Transjugular intrahepatic portosystemic shunt; anticoagulation therapy; hepatic vein outflow tract obstruction; transjugular intrahepatic portosystemic shunt

Abstract

Intra-hepatic portal-venous collaterals are characteristic of Budd-Chiari syndrome (BCS) and are usually of small caliber and seen on Doppler. Creation of large portal-systemic shunt, either radiologically (Transjugular intrahepatic porto-systemic shunt) or surgically results in excellent long term outcomes in BCS. Here, we report a series of three rare cases of asymptomatic BCS, who had spontaneous large intra-hepatic portal-systemic shunts.

摘要

肝内门静脉络脉是Budd-Chiari综合征（BCS）的特征，通常是小口径的，在多普勒上可见。建立大型门静脉系统分流术，放射学（经颈静脉肝内门体分流术）或手术均可在BCS中获得出色的长期结果。这里,我们报告了三例罕见的无症状BCS，有自发性大型肝内门静脉系统分流。