背景:输精管可能表现为各种异常,例如不存在,重复,异位,或憩室。异位精道开口主要有两种类型,异位射精管开口,和异位输精管开放。一般来说,输精管异常影响约0.05%的人口。患者可能无症状或抱怨尿路感染和/或附睾炎。这些病例中的大多数与肾发育不良有关。为了明确诊断,应进行膀胱尿道镜检查导管插入术和逆行尿道造影,但最终的诊断是通过血管造影来完成的.最终的治疗方法是病理性泌尿生殖系统连接的完全手术切除。这种情况通常是在探索其他发现时发现的,例如睾丸扭转和腹股沟疝。
方法:我们报告了一例罕见的11岁男性,表现为肉眼血尿和许多先天性畸形,包括左多指畸形。多睾丸,有几个外科手术,左肾发育不全。左腹股沟疝手术,在此期间,偶然发现了第三个未降睾丸并将其根除。进行逆行尿道造影以建立诊断。切除了与左输尿管相连的瘘管。组织病理学结果证实了输精管的真实重复的诊断,输尿管和输精管之间的通信。通过后续行动,肾功能检查在正常范围内.
结论:本病例报告旨在强调重复输精管和相关先天性畸形的早期诊断和治疗,以改善预后和肾功能,避免长期并发症。
BACKGROUND: Ductus deferens may manifest in a variety of anomalies such as its absence, duplication, ectopy, or diverticulum. Ectopic seminal tract opening has two main types, ectopic ejaculatory duct opening, and ectopic vas deferens opening. Generally, ductus deferens anomalies affect approximately 0.05% of the population. Patients may be asymptomatic or complaining of urinary tract infections and/or epididymitis. Most of these cases are associated with renal dysplasia. To confirm the diagnosis Cystourethroscopy catheterization and retrograde urethrogram should be performed, but the definitive diagnosis is done by vasography. The definitive treatment is complete surgical resection of the pathological urogenital connection. This
case is commonly discovered while exploring other findings such as testicular torsion and inguinal hernia.
METHODS: We report a rare
case of an 11-year-old male who presented with gross hematuria and numerous congenital malformations including a left polydactyly clubfoot, polyorchidism, with several surgical procedures, and left kidney dysgenesis. Surgery was performed for a left inguinal hernia, during which a third undescended testicle was discovered incidentally and was eradicated. A retrograde urethrogram was performed to establish the diagnosis. A fistula- that is connected with the left ureter- was resected. The histopathologic findings confirmed the diagnosis of true duplication of the Vas deferens, with communication between the ureter and the vas deferens. By follow-up, the kidney function tests were within normal limits.
CONCLUSIONS: This
case report aims to highlight the early diagnosis and management of the duplicated vas deferens and the associated congenital malformations to improve the prognosis and kidney function and to avoid long-term complications.