Abstract：
Nutrition has played a central role in the management and outcomes of people with cystic fibrosis (pwCF) since the 1970s. Advances in therapies and practices in recent decades have led to a significant change in the patient landscape with dramatic improvements in life expectancy, as well as quality of life, bringing with it new issues. Historically, cystic fibrosis was a condition associated with childhood and malnutrition; however, changes in patient demographics, nutritional assessment and fundamental nutritional management have evolved, and it has become an increasingly prevalent adult disease with new nutritional challenges, including obesity. This paper aims to describe these changes and the impact and challenges they bring for those working in this field. Nutritional professionals will need to evolve, adapt and remain agile to the wider range of situations and support required for a new generation of pwCF. Specialised nutrition support will continue to be required, and it will be additionally important to improve and optimise quality of life and long-term health.
摘要：
自1970年代以来，营养在囊性纤维化（pwCF）患者的管理和结果中发挥了核心作用。近几十年来，治疗和实践的进步导致患者景观发生了重大变化，预期寿命显着提高。以及生活质量，带来新的问题。历史上,囊性纤维化是一种与儿童和营养不良有关的疾病;然而,患者人口统计学的变化，营养评估和基本营养管理已经发展，它已经成为一种越来越普遍的成人疾病，面临着新的营养挑战，包括肥胖.本文旨在描述这些变化以及它们为该领域的工作人员带来的影响和挑战。营养专业人员需要进化，适应并保持敏捷适应新一代pwCF所需的更广泛的情况和支持。将继续需要专门的营养支持，此外，改善和优化生活质量和长期健康也很重要。
