Abstract：
Dural sinus malformation (DSM) is a rare vascular malformation characterized by the dilatation of a dural venous sinus with or without an anomalous jugular bulb. Its presentation with venous-reflux-related secondary proptosis is anecdotal, with only six such cases reported so far. We report a 17-month-old boy who presented with a progressive proptosis of the right eye secondary to a DSM of the transverse sinus and torcula. Following endovascular embolization of the arterio-venous fistula, complete thrombosis of the venous lake and improvement in proptosis was noted at 6-month follow-up. Prognosis of this rare malformation is variable and dependent on specific angio-architectural features.
摘要：
硬脑膜窦畸形（DSM）是一种罕见的血管畸形，其特征是硬脑膜静脉窦扩张，有或没有异常的颈静脉球。它的表现与静脉反流相关的继发性突增是轶事，到目前为止，只有6起此类病例报告。我们报告了一个17个月大的男孩，该男孩在横窦和耳廓的DSM之后表现出右眼进行性突出。动静脉瘘血管内栓塞后，在6个月的随访中发现静脉湖完全血栓形成和眼球突出改善.这种罕见畸形的预后是可变的，并取决于特定的血管结构特征。
