Abstract：
Caroli\'s disease is also known as Congenital intrahepatic bile duct dilatation, and previously known as a congenital intrahepatic bile duct cyst; it is characterized by single or multiple intrahepatic cystic dilatations. In this article, we report a case of Caroli\'s disease (CT size 21.2 × 16.9 × 19.8 cm). Preoperative abdominal ultrasound and enhanced CT were misdiagnosed as biliary cystadenoma or hepatic echinococcosis, and finally diagnosed as Caroli\'s disease by postoperative histopathological examinations. Most of the disease is single or multiple cystic dilatation of small bile duct. Giant Caroli disease, cystic dilations with diameter >20 cm is very rarely seen in the clinic. The lack of experience of diagnosing giant cystic dilatation makes it difficult to make accurate diagnosis. Therefore, we analyze the causes of imaging misdiagnosis through this case report, and summarize the imaging diagnostic skills of the disease combined with relevant imaging diagnosis experience. The purpose of this study is to deepen the understanding of giant Caroli disease among imaging doctors so as to reduce the misdiagnosis of the disease in the future.
摘要：
Caroli病也被称为先天性肝内胆管扩张症，以前称为先天性肝内胆管囊肿；它的特征是单个或多个肝内囊性扩张。在这篇文章中,我们报告了1例Caroli病（CT大小21.2×16.9×19.8cm）。术前腹部超声和增强CT误诊为胆管囊腺瘤或肝包虫病，最后通过术后组织病理学检查确诊为Caroli病。大多数疾病是单发或多发的小胆管囊性扩张。巨大的Caroli病,直径>20厘米的囊性扩张在临床上很少见。缺乏诊断巨大囊性扩张的经验，难以做出准确的诊断。因此,通过本病例报告分析影像学误诊的原因,结合相关影像学诊断经验,总结该病的影像学诊断技巧。本研究旨在加深影像学医师对巨大Caroli病的认识,减少今后对该病的误诊。
