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Abstract：
Primary Angiitis of the Central Nervous System (PACNS) is a rare disease and its diagnosis is a challenge for several reasons, including the lack of specificity of the main findings highlighted in the current diagnostic criteria. Among the neuroimaging pattern of PACNS, a tumefactive form (t-PACNS) is a rare subtype and its differential diagnosis mainly relies on neuroimaging. Tumor-like mass lesions in the brain are a heterogeneous category including tumors (in particular, primary brain tumors such as glial tumors and lymphoma), inflammatory (e.g., t-PACNS, tumefactive demyelinating lesions, and neurosarcoidosis), and infectious diseases (e.g., neurotoxoplasmosis). In this review, the main features of t-PACNS are addressed and the main differential diagnoses from a neuroimaging perspective (mainly Magnetic Resonance Imaging-MRI-techniques) are described, including conventional and advanced MRI.
摘要：
原发性中枢神经系统（PACNS）是一种罕见的疾病，其诊断是一个挑战，有几个原因，包括当前诊断标准中强调的主要发现缺乏特异性。在PACNS的神经影像学模式中，肿瘤分型(t-PACNS)是一种罕见亚型,其鉴别诊断主要依靠神经影像学.脑中的肿瘤样肿块病变是一个异质性类别，包括肿瘤（特别是，原发性脑肿瘤，如神经胶质肿瘤和淋巴瘤），炎性(例如，t-PACNS,肿瘤性脱髓鞘性病变，和神经结节病)，和传染病(例如，神经弓形虫病）。在这次审查中,解决了t-PACNS的主要特征，并描述了从神经影像学角度（主要是磁共振成像-MRI技术）的主要鉴别诊断，包括常规和高级MRI.
