Abstract:
Rhabdomyosarcoma (RMS) is the most common soft-tissue sarcoma in children. The present study reports the case of a 2-year-old female who presented with abdominal pain and a palpable abdominal mass. Radiological investigations failed to reveal the tissue origin of the mass and a tru-cut biopsy confirmed the diagnosis of embryonal RMS. Surgical excision was performed after neo-adjuvant chemotherapy. The pelvic end of the mass was observed to continue with the left medial umbilical ligament. The patient\'s postoperative course was uneventful, and follow-up imaging showed no evidence of recurrence. Τhe present case report is the first non-syndromic case with left umbilical medial ligament-originated RMS.
摘要:
横纹肌肉瘤(RMS)是儿童最常见的软组织肉瘤。本研究报告了一名2岁女性的病例,该女性表现出腹痛和明显的腹部肿块。放射学检查未能揭示肿块的组织起源,切开的活检证实了胚胎RMS的诊断。新辅助化疗后进行手术切除。观察到肿块的骨盆端与左脐内侧韧带延续。病人的术后过程是顺利的,随访影像学显示无复发证据.本病例报告是第一例左脐内侧韧带起源RMS的非综合征病例。