PDF(Pubmed)
Abstract：
Fibrous dysplasia is a benign, developmental bone disorder that causes fibrous replacement of normal skeletal tissue. This may lead to weakness, distortion, and tissue expansion. Fibrous dysplasia can occur anywhere in the body, including the craniofacial area. The clivus is a central skull bone formed by the bases of the sphenoid and occiput, respectively. The clivus is a rare, usually unrecognized, and seldom reported location for the development of fibrous dysplasia. Although fibrous dysplasia of the clivus (FDC) is usually discovered by incidental findings, it can sometimes present with clinical symptoms. In this case, we discuss a 30-year-old male who presents to the emergency room with headaches, altered mental status, and a prior presentation of location-related symptomatic epilepsy. Magnetic resonance imaging depicted a mass in the clivus, low in signal on T1 and mildly hypointense on T2 imaging. Follow-up computed tomography (CT) imaging, as recommended, revealed the classic presentation of FDC. In this paper, we discuss the significance of this condition and the importance of thorough investigation to rule out differential diagnoses that may present with similar acute symptoms as this patient.
摘要：
纤维发育不良是良性的，导致正常骨骼组织纤维替代的发育性骨骼疾病。这可能会导致软弱，失真，和组织扩张。纤维发育不良可以发生在身体的任何地方，包括颅面区域.clivus是由蝶骨和枕骨的基部形成的中央颅骨，分别。气候是一种罕见的，通常无法识别，很少报道纤维发育不良的位置。尽管斜坡的纤维发育不良（FDC）通常是偶然发现的，有时会出现临床症状。在这种情况下,我们讨论了一个30岁的男性，他头痛地出现在急诊室，精神状态改变,和位置相关症状性癫痫的先前表现。磁共振成像描绘了悬崖上的肿块，T1信号低，T2成像信号轻度低。后续计算机断层扫描（CT）成像，如建议,揭示了FDC的经典演示。在本文中,我们讨论了这种情况的重要性，以及彻底调查以排除可能与该患者类似的急性症状的鉴别诊断的重要性。
