PDF(Pubmed)
Abstract：
BACKGROUND: A pseudoaneurysm of the superficial temporal artery is an uncommon clinical entity that has largely been linked with direct traumatic causes. Neurofibromatosis type 1 (NF1)-related vasculopathy is a rare cause of idiopathic arterial bleeding in the craniofacial region.
METHODS: A 46-year-old male with clinical features of NF1 presented to the hospital with an enlarging and tender right temporal mass without a history of trauma. Computed tomography angiography suggested the development of a pseudoaneurysm, and surgery was performed to resect the mass. Histopathological examinations showed focal interruption of the epithelium layer and elastic lamina, well-demarcated thickening of the smooth muscle layers of the arterial wall, supporting the diagnosis of pseudoaneurysm.
CONCLUSIONS: NF1-associated vasculopathy is likely the predisposing factor for the development of a superficial temporal artery pseudoaneurysm.
METHODS: A 46-year-old male with clinical features of NF1 presented to the hospital with an enlarging and tender right temporal mass without a history of trauma. Computed tomography angiography suggested the development of a pseudoaneurysm, and surgery was performed to resect the mass. Histopathological examinations showed focal interruption of the epithelium layer and elastic lamina, well-demarcated thickening of the smooth muscle layers of the arterial wall, supporting the diagnosis of pseudoaneurysm.
CONCLUSIONS: NF1-associated vasculopathy is likely the predisposing factor for the development of a superficial temporal artery pseudoaneurysm.
摘要：
背景：颞浅动脉假性动脉瘤是一种罕见的临床实体，在很大程度上与直接的创伤原因有关。1型神经纤维瘤病（NF1）相关的血管病变是颅面区域特发性动脉出血的罕见原因。
方法：一名46岁男性，其临床特征为NF1，患者右侧颞部肿块扩大，触痛，无外伤史。计算机断层扫描血管造影提示假性动脉瘤的发展，并进行手术切除肿块。组织病理学检查显示上皮层和弹性层的局灶性中断，清晰的动脉壁平滑肌层增厚，支持假性动脉瘤的诊断.
结论：NF1相关血管病变可能是颞浅动脉假性动脉瘤发展的诱发因素。
方法：一名46岁男性，其临床特征为NF1，患者右侧颞部肿块扩大，触痛，无外伤史。计算机断层扫描血管造影提示假性动脉瘤的发展，并进行手术切除肿块。组织病理学检查显示上皮层和弹性层的局灶性中断，清晰的动脉壁平滑肌层增厚，支持假性动脉瘤的诊断.
结论：NF1相关血管病变可能是颞浅动脉假性动脉瘤发展的诱发因素。
