%0 Journal Article %T Spontaneous pseudoaneurysm of the superficial temporal artery in neurofibromatosis type 1: illustrative case. %A Shen F %A Li SZ %A Shan YY %A Ji X %A Sheng HS %J J Neurosurg Case Lessons %V 6 %N 14 %D 2023 Oct 2 %M 37782958 暂无%R 10.3171/CASE23384 %X BACKGROUND: A pseudoaneurysm of the superficial temporal artery is an uncommon clinical entity that has largely been linked with direct traumatic causes. Neurofibromatosis type 1 (NF1)-related vasculopathy is a rare cause of idiopathic arterial bleeding in the craniofacial region.
METHODS: A 46-year-old male with clinical features of NF1 presented to the hospital with an enlarging and tender right temporal mass without a history of trauma. Computed tomography angiography suggested the development of a pseudoaneurysm, and surgery was performed to resect the mass. Histopathological examinations showed focal interruption of the epithelium layer and elastic lamina, well-demarcated thickening of the smooth muscle layers of the arterial wall, supporting the diagnosis of pseudoaneurysm.
CONCLUSIONS: NF1-associated vasculopathy is likely the predisposing factor for the development of a superficial temporal artery pseudoaneurysm.