PDF(Pubmed)
Abstract：
An 87-year-old man presented with dyspnea. Computed tomography revealed progressive subpleural consolidation in the apex, reticular shadows in the lower lobes, and bilateral ground glass opacifications. He died of respiratory failure on day 3. The post-mortem examination showed exudative stage diffuse alveolar damage and pulmonary edema. Intraalveolar collagenous fibrosis and subpleural elastosis were observed in the upper lobes, accompanied by interlobular septal and pleural thickening and lung architecture remodeling in the lower lobes. He was diagnosed with acute exacerbation of pleuroparenchymal fibroelastosis with lower lobe usual interstitial pneumonia, which can be fatal.
摘要：
一名87岁男子出现呼吸困难。计算机断层扫描显示心尖区进行性胸膜下实变，下叶的网状阴影，和双侧毛玻璃混浊。他在第3天死于呼吸衰竭。尸检显示渗出性弥漫性肺泡损伤和肺水肿。在上叶观察到肺泡内胶原性纤维化和胸膜下弹性增生，伴有小叶间隔和胸膜增厚以及下叶的肺结构重塑。他被诊断为胸膜实质纤维弹性增生症急性加重并下叶普通间质性肺炎,这可能是致命的。
