关键词: Alveolar soft part sarcoma Exenteration Histopathology Imaging Immunohistochemistry Orbit

来  源:   DOI:10.1016/j.ajoc.2022.101645   PDF(Pubmed)

Abstract:
UNASSIGNED: Alveolar soft part sarcoma (ASPS) is a very rare type of soft tissue sarcomas which usually occurs in the limbs and trunk.
UNASSIGNED: A 25-year-old woman presented with proptosis and redness of the right eye for 8-month. She suffered from severe right upper lid edema, conjunctival chemosis, downward displacement of the globe, and proptosis. Radiological imaging was nonconclusive. Histopathological evaluations confirmed ASPS. The patient underwent exenteration as a lifesaving procedure. At 16-month follow-up, the patient is stable without any signs of recurrence or metastasis.
UNASSIGNED: We report an extremely rare case of ASPS occurring in the superior rectus muscle. Few orbital ASPS cases have been reported in the literature. A literature review of orbital ASPS was done to shed lights on the diagnosis and management of this rare tumor.
摘要:
肺泡软组织肉瘤(ASPS)是一种非常罕见的软组织肉瘤,通常发生在四肢和躯干。
一名25岁的女性出现8个月的眼球突出和右眼发红。她患有严重的右上眼睑水肿,结膜化学,地球的向下位移,和突起。放射学成像是非决定性的。组织病理学评估证实了ASPS。患者接受了作为挽救生命的手术。在16个月的随访中,患者病情稳定,无复发或转移迹象。
我们报告了一例发生在上直肌的非常罕见的ASPS病例。文献中很少报道眼眶ASPS病例。对眼眶ASPS进行了文献综述,以阐明这种罕见肿瘤的诊断和治疗。
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