Abstract：
Juvenile xanthogranuloma, a form of non-Langerhans cell histiocytosis can be defined as the proliferation of cells with macrophage like characteristics. It has been described as a benign, asymptomatic and common self-healing disorder of non-Langerhans cell histiocytosis (LCH), affecting mostly infants, children and rarely adults. We have documented a case of a 40 year old male who presented to us with extensive insidious papulonodulous growth over the face. The facial disfigurement caused was catastrophic. An extensive surgical excision and reconstruction was performed followed by histopathological evaluation. Microscopic study and immune histochemistry revaled Juvenile Xanthogranuloma of adult. The article highlights the presentation, diagnosis and management of this mammoth, rare disease.
摘要：
青少年黄色肉芽肿，非朗格汉斯细胞组织细胞增生症的一种形式可以定义为具有巨噬细胞样特征的细胞的增殖。它被描述为良性的，无症状和常见的非朗格汉斯细胞组织细胞增生症（LCH）的自愈障碍，主要影响婴儿，儿童，很少成人。我们已经记录了一例40岁的男性，他向我们展示了面部广泛阴险的丘疹样生长。造成的面部毁容是灾难性的。进行了广泛的手术切除和重建，然后进行了组织病理学评估。成人青少年黄色肉芽肿的显微研究和免疫组织化学研究。文章重点介绍了演示文稿，这只猛犸象的诊断和管理，罕见病
