%0 Case Reports
%T Giant Juvenile Xanthogranuloma of face in an adult: A rare complexity.
%A Richardson S
%A Banerjee P
%A Hassan MES
%A Mobarak FA
%J J Stomatol Oral Maxillofac Surg
%V 123
%N 5
%D Oct 2022
%M 35395418
%F 2.48
%R 10.1016/j.jormas.2022.03.019
%X Juvenile xanthogranuloma, a form of non-Langerhans cell histiocytosis can be defined as the proliferation of cells with macrophage like characteristics. It has been described as a benign, asymptomatic and common self-healing disorder of non-Langerhans cell histiocytosis (LCH), affecting mostly infants, children and rarely adults. We have documented a case of a 40 year old male who presented to us with extensive insidious papulonodulous growth over the face. The facial disfigurement caused was catastrophic. An extensive surgical excision and reconstruction was performed followed by histopathological evaluation. Microscopic study and immune histochemistry revaled Juvenile Xanthogranuloma of adult. The article highlights the presentation, diagnosis and management of this mammoth, rare disease.