PDF(Pubmed)
Abstract：
A holocord syringomyelia due to Chiari 1.5 malformation (CM) in a 12-year-old girl was serially imaged with 3 T MRI over 4 years. The serial MRI showed reduction in size of the syrinx, without any surgical intervention or CM improvement, but rather due to spontaneous spinal cord tear. The tear was clearly demonstrated by evidence of flow signal across the tear between syrinx and subarachnoid space at the upper thoracic level. The tear showed spontaneous closure at follow-up. A medullary tear has been described in the adult population as one of the putative causes of spontaneous syringomyelia reduction, but its clear demonstration with modern high-resolution MRI has not been reported in the paediatric population. Moreover, this is the first reported case of syrinx reduction due to spontaneous fissuration in a paediatric patient.
摘要：
对一名12岁女孩因Chiari1.5畸形（CM）引起的全脊髓空洞症进行了4年的3TMRI连续成像。系列MRI显示注射器的尺寸减小，没有任何手术干预或CM改善，而是由于自发性脊髓撕裂.通过胸上水平的syrinx和蛛网膜下腔之间的撕裂处的血流信号的证据清楚地证明了撕裂。泪液在随访时表现为自发闭合。成人中的髓质撕裂已被描述为自发性脊髓空洞症减少的推定原因之一，但在儿科人群中尚未报道现代高分辨率MRI的清晰演示。此外，这是首例报道的儿科患者由于自发性裂隙而导致的syrinx减少病例.
