Wide QRS in a 2-month infant associated with recurrent ventricular tachycardia: A case of Brugada-like syndrome.

• 发表时间: Feb 2017
• 来源期刊: Ann Cardiol Angeiol (Paris)
• DOI: 10.1016/j.ancard.2016.12.005
• PMID: 28139199
• 文章类型: Case Reports
• 作者列表: Jomaa W,Selmi W,Hamdi S,Azaiez MA,El Hraiech A,Ben Hamda K,Maatouk F

关键词: Brugada syndrome; Infant; Nourrisson; Syndrome de Brugada; Tachycardie ventriculaire; Ventricular tachycardia

Mesh: Brugada Syndrome / diagnosis genetics; Bundle-Branch Block / diagnosis genetics; DNA Mutational Analysis; Diagnosis, Differential; Electrocardiography; Humans; Infant; Male; Recurrence; Sodium Channels / genetics; Tachycardia, Ventricular / diagnosis genetics

Abstract

We report the case of a 2-month old infant who experienced recurrent sustained ventricular tachycardia (VT) in a structurally normal heart. Resting electrocardiogram (ECG) showed wide QRS with a complete right bundle branch bloc (RBBB) morphology. There was no family history of syncope or sudden death, but the ECGs of the father and the brother showed incomplete RBBB with negative T waves on V1 lead. This case seems to fit well with the newly defined entity of Brugada-like syndrome with a highly suspected genetic underlying disposition.