SSc中的心脏病可以以各种方式表现并且与不良预后相关。关于如何在SSc中最好地检测和管理心脏病的证据很少。我们的目标是为SSc中的心脏病管理提供专家共识的最佳实践途径。
英国系统性硬化症研究小组成立了几个工作组,以开发一些共识的最佳实践途径来管理SSc特异性并发症。包括心脏病.召集了一个多学科工作队。该指南部分是由全面的文献综述提供的。
介绍了SSc中心脏病(重点是原发性心脏病)的最佳实践途径,包括早期检测和标准药物和设备治疗的方法。由于好处,建议采用共同护理和多学科方法。针对该倡议强调的对原发性心脏病自然史的了解相对缺乏,已经制定了未来的研究议程。
医生应警惕SSc中心脏病的可能性;最好在包括风湿病专家和心脏病专家在内的多学科团队中进行管理。该途径为所有医生管理SSc患者提供了参考。
Cardiac disease in SSc can manifest in various ways and is associated with a poor prognosis. There is little evidence on how best to detect and manage cardiac disease in SSc. Our objective was to produce an expert consensus best practice pathway for the management of cardiac disease in SSc.
The UK Systemic Sclerosis Study Group set up several working groups to develop a number of consensus best practice pathways for the management of SSc-specific complications, including cardiac disease. A multidisciplinary task force was convened. The guidelines were partly informed by a comprehensive literature review.
A best practice pathway for cardiac disease (with a focus on primary cardiac disease) in SSc is presented, including approaches for early detection and standard pharmacological and device therapies. Due to the benefits, shared care and a multidisciplinary approach are recommended. A future research agenda has been formulated in response to the relative lack of understanding of the natural history of primary cardiac disease that was highlighted by the initiative.
The physician should be alert to the possibility of cardiac disease in SSc; it is best managed within a multidisciplinary team including both rheumatologists and cardiologists. This pathway provides a reference for all physicians managing patients with SSc.