背景:先天性锁骨假关节(CPC)是一种罕见的先天性实体,病因和发病机制尚未解决。迄今为止,已报告了近250例病例。CPC的特征是出生时锁骨中部有明确的缺陷,通常在儿童后期或青春期畸形明显时被诊断出来。手术管理是有争议的,尤其是无症状儿童,与文献中报道的各种技术。
方法:我们报告了一例6岁男孩在小学入学体检时被诊断为CPC的病例。手术治疗包括假关节病清创术,第三管板内固定,和桶形单皮质髂骨自体移植。
结果:术后9个月获得完整的骨愈合,术后4年和3个月观察到令人满意的功能和外观。
结论:我们认为,采用桶形单皮质髂棘自体移植重建是治疗CPC的一种有效且可重复的手术技术。
BACKGROUND: Congenital pseudarthrosis of the clavicle (CPC) is a rare congenital entity with unresolved aetiology and pathogenesis. Nearly 250 cases have been reported to date. CPC is characterized by a definite defect in the mid-clavicle at birth and is usually diagnosed when the deformity becomes evident in late childhood or adolescence. Surgical management is controversial, especially in asymptomatic children, with various techniques reported in the literature.
METHODS: We report a case of a 6-year-old boy who was diagnosed with CPC during a medical examination for primary school enrollment. Operative treatment included debridement of pseudoarthrosis, internal fixation with third tube plate, and barrel-shaped mono-cortical iliac crest autograft.
RESULTS: A complete bone union was obtained 9 months after the operation, and satisfactory function and cosmetic appearance were observed 4 years and 3 months postoperatively.
CONCLUSIONS: In our opinion, reconstruction with barrel-shaped mono-cortical iliac crest autograft was an effective and reproducible surgical technique to treat CPC.