据报道,每年约有2,000例脂肪肉瘤的发病率约占粘液样脂肪肉瘤的30%。心脏肌氧脂肪肉瘤非常罕见;它们的表现可能是心脏填塞,由于肿瘤和/或心包积液的直接压迫。在这份报告中,我们描述了一名患者,他出现了继发于右心房的myoxid脂肪肉瘤的心包积液,脂肪肉瘤在心脏中极为罕见。我们还通过超声心动图提供非侵入性成像,CECT胸部和FDGPET扫描,然后进行CT引导下的肿块活检。右心房肿块的组织病理学显示,粘液样脂肪肉瘤对S100肿瘤标志物呈阳性。
The reported incidence of liposarcomas in ~2,000 cases annually results in about 30% of myxoid liposarcomas. Cardiac myoxid liposarcomas are very rare; their presentation could be cardiac tamponade, due to direct compression of the tumor and/or pericardial effusion. In this report, we describe a patient who presented with pericardial effusion secondary to myoxid liposarcomas from the right atrium, an extremely rare presentation of liposarcomas in the heart. We also present non-invasive imaging through echocardiography, CECT thorax and FDG PET scans, followed by a CT-guided mass biopsy. Histopathology of the right atrial mass demonstrated myxoid liposarcoma positive for the S100 tumor marker.