成人起病静症(AOSD)是一种罕见的自身炎症性疾病,表现出广泛的非特异性症状,而budd-chiari综合征(BCS)是一种罕见的疾病,其特征是肝静脉流出道阻塞。我们介绍了一名年轻患者持续发烧的情况,喉咙痛,弯头,手手指和膝盖关节痛伴腹痛。患者的症状在转诊前7天开始。影像学和实验室数据导致AOSD背景下BCS的诊断。患者接受皮质类固醇联合华法林治疗,结果良好,体征和症状得到完全改善。我们得出这个结论AOSD与BCS并发是一种罕见但可能危及生命的实体。临床医生应该意识到这种并发症。
Adult onset still\'s disease (AOSD) is a rare autoinflammatory disease displaying with a wide range of non-specific symptoms and budd-chiari syndrome (BCS) is an uncommon disorder characterized by obstruction of hepatic venous outflow. We present the case of a young patient who presented with persistent fever, sore throat, elbow, hand fingers and knees arthralgia with abdominal pain. The patient\'s symptoms had started 7 days before the referral. Imaging and laboratory data led to the diagnosis of BCS in the context of AOSD. The patient treated with corticosteroid in combination of warfarin with favorable outcome and complete improvement of signs and symptoms. We came to this conclusion AOSD complicated with BCS is a rare but potentially life-threatening entity. Clinicians should be aware of this complication.