Urethral duplication

尿道重复
  • 文章类型: Case Reports
    尿道重复是一种先天性异常,其特征是辅助尿道的部分或全部发育为第二尿道通道,其范围和位置各不相同。尿道重复的治疗过程应根据异常的类型和症状的存在为每个患者个体化。在大多数情况下,如果腹侧原位尿道正常,背侧辅助尿道的切除几乎总是有疗效的。
    方法:我们报告一例13岁男孩反复尿路感染,偶尔在阴茎轴背侧的外部针孔孔孔孔处有尿液滴。进行了几项调查以确认背侧附件尿道的存在。患者接受了附件尿道的完全切除,术后12周,患者完全无症状.
    结论:尿道重复是罕见的异常。这些异常在文献中以各种方式进行了分类,包括矢状和侧向重复,背侧和腹侧重复。矢状面是大多数尿道重复发生的地方。根据解剖变异,临床表现和异常的严重程度,尿道重复治疗应该为每个病人定制。无症状儿童可能不需要特殊治疗。背侧附件尿道的完全手术切除似乎提供了最佳的治疗解决方案。
    结论:当腹侧原位尿道正常时,背侧副尿道切除术通常是治愈的。必须在手术前进行彻底的检查以确定尿道重复的类型。尿道重复症最常见的诊断程序包括膀胱镜检查,KUB超声检查,和膀胱尿道造影。这些程序可以帮助计划手术,预防并发症,如神经血管束损伤和尿失禁,提高患者的自尊和生活质量。
    UNASSIGNED: Urethral duplication is a congenital anomaly characterized by the partial or full development of an auxiliary urethra as a second urethral channel varying in extent and location. The course of treatment for urethral duplication should be individualized for each patient based on the type of anomaly and the existence of symptoms. In most cases, if the ventral orthotopic urethra is normal, excision of the dorsal auxiliary urethra is almost always curative.
    METHODS: We report a case of a 13-year-old boy who presented with recurrent urinary tract infection, occasionally having drops of urine at an external pin hole meatal opening on the dorsum of the penile shaft. Several investigations were performed to confirm the presence of the dorsal accessory urethra. The patient underwent complete excision of the accessory urethra, and 12 weeks post-surgery the patient was completely asymptomatic.
    CONCLUSIONS: Urethral duplications are rare anomalies. These anomalies have been classified in various ways in the literature, including sagittal and lateral duplications, dorsal and ventral duplications. The sagittal plane is where the majority of urethral duplications occur. Based on the anatomic variation, clinical presentation and severity of the anomaly, urethral duplication treatment should be customized for each patient. An asymptomatic child may require no specific treatment. Total surgical excision of the dorsal accessory urethra appears to offer the best curative solution.
    CONCLUSIONS: Excision of the dorsal accessory urethra is usually curative when the ventral orthotopic urethra is normal. Thorough investigation before surgery is mandatory to determine the type of urethral duplication. The most common diagnostic procedures for urethral duplications include cystoscopy, KUB ultrasonography, and micturating cystourethrography. These procedures can help plan surgery, prevent complications such as neurovascular bundle injuries and urine incontinence, and improve patient self-esteem and quality of life.
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  • 文章类型: Case Reports
    尿道重复是具有多种解剖变体的多种疾病。临床表现从无症状到复发性尿路感染不等。需要主要护理人员的高度临床怀疑和意识才能做出正确的诊断。应评估所有患有任何阴茎畸形或尿流异常的患者,以排除这种情况。在这种情况下,由于附件尿道的束缚,阴茎的背侧弯曲异常,患者出现了朝向腹部的尿流。
    Urethral duplication is a diverse spectrum of disease having multiple anatomic variants. The clinical presentation varies from being asymptomatic to recurrent urinary tract infections. A high level of clinical suspicion and awareness among primary caregivers is needed to make a proper diagnosis. All patients presenting with any sort of penile deformity or abnormality of the urinary stream should be evaluated to rule out this condition. In this case report the patient had presented with the urinary stream being directed towards his abdomen due to abnormal dorsal curvature of the penis which was due to tethering of the accessory urethra.
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  • 文章类型: Journal Article
    背景:报告一种用于处理IIA1型尿道重复(UD)的端到侧尿道-尿道造口术的新方法。
    方法:一名3岁男孩因生殖器异常外观而被转诊到我们研究所。体格检查显示阴茎干背侧有一个上下颌道,除了龟头尖端的原位鼻道。他可以通过尿道排便(I级)。排尿膀胱尿道造影和膀胱镜检查证实IIA1型UD有两个尿道独立于膀胱颈。成功进行了一种新颖的端到侧尿道尿道造口术,将背侧尿道通过海绵体转移并吻合到腹侧尿道后壁。
    结果:术后2周拔除导尿管。未发现尿道狭窄和瘘管。经过1年的随访,这个男孩可以流利地排尿(I级)。Qmax为10.4ml/s。
    结论:我们采用端侧尿道-尿道造口术治疗IIA1型UD是安全有效的,特别是对于阴茎轴上有异位鼻道的大陆病例。
    To report a novel maneuver of end-to-side urethro-urethrostomy for managing Type IIA1 urethral duplication (UD).
    A 3-years-old boy was referred to our institute for abnormal appearance of genitalia. Physical examination revealed an epispadiac meatus on the dorsum of the penile shaft, in addition to the orthotopic meatus at the tip of glans. He can void through both urethrae with continence (grade I). Voiding cystourethrography and the cystoscopy confirmed the Type IIA1 UD with two urethrae arising independently from the bladder neck. A novel maneuver of end-to-side urethro-urethrostomy transferring the dorsal urethra through the corpus cavernosa and anastomosing it to the posterior wall of the ventral urethra was successfully performed.
    The urethral catheter was removed 2 weeks postoperatively. Neither urethral stricture nor fistula was noticed. After 1 year of followed-up, the boy can void fluently with continence (grade I). The Qmax was 10.4 ml/s.
    Our maneuver of end-to-side urethro-urethrostomy for managing Type IIA1 UD was safe and effective, especially for the continent cases with the ectopic meatus on the penile shaft.
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  • 文章类型: Case Reports
    尿道重复是一种罕见的异常,临床表现各不相同。迄今为止,已报告约300例病例,通常与泌尿生殖道(GU)和胃肠道(GI)异常有关。一名6天大的新生儿,肛门开口缺失,会阴瘘微小,有轻微的胎粪染色。他在肛门成形术后做得很好。据报道,低肛门直肠畸形(ARM)是与尿道重复有关的胃肠道异常。然而,在文献中首次报道异位阴囊是与尿道重复相关的主要GU道异常,并有可能的胚胎学解释。GU束异常在婴儿期后期通过手术成功修复。
    Urethral duplication is a rare anomaly with varying clinical manifestations. About 300 cases have been reported till date and are often associated with genitourinary (GU) and gastrointestinal (GI) tract anomalies. A 6-day-old neonate presented with an absent anal opening and a tiny perineal fistula having slight meconium staining. He did well after anoplasty. Low anorectal malformation (ARM) has been reported as the GI anomaly associated with urethral duplication. However, an ectopic scrotum as the principal GU tract anomaly associated with urethral duplication is being reported for the first time in literature with probable embryologic explanation. The GU tract anomalies were successfully repaired surgically later in infancy.
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  • 文章类型: Case Reports
    尿道重复是下尿路的罕见异常,由男性比女性常见的辅助尿道的部分或完全发育组成。这种情况的确切胚胎机制尚不清楚,它被认为与后肠发育过程中Rathke外侧褶皱的发育中断有关。根据Effman\的分类有3种类型。尿道重复的诊断,必须进行生殖器检查,并通过排尿膀胱尿道造影和逆行尿道造影进行确认。作者介绍了一例67岁男子抱怨排尿困难,进行逆行尿道造影和排尿膀胱尿道造影后,被诊断为尿道重复Effman分类IIB型并伴有球尿道狭窄和憩室以及多个膀胱憩室。这是一种非常罕见的尿道重复(IIB型),表现较晚。关于手术管理可能需要进一步的研究。
    Urethral duplication are rare anomalies of the lower urinary tract consisting of partial or complete development of an accessory urethra that common in males than female. The exact embryological mechanism for this condition remain unclear, it is thought to relate to a disruption of development of the lateral folds of Rathke during hindgut development. There are 3 types based on Effman\'s classification. Diagnosis of urethral duplication, a genital examination has to performed and confirmed by micturating cytourethrography and retrograde urethrography. The authors presented a case of 67-year-old man complaining of dysuria, who was diagnosed with urethral duplication Effman Classification type IIB accompanied by bulbar urethral stricture and diverticula and multiple bladder diverticula after performing retrograde urethrography and micturating cystourethrography. This is an extremely rare type of duplication of the urethra (type IIB) with late presentation. Further study may be required regarding the surgical management.
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  • 文章类型: Case Reports
    尿道重复是一种罕见的疾病,具有多种临床症状,在男性中更为常见;仅报道了少于300例。在这个案例报告中,一名20岁的男性患者来到泌尿科综合诊所,龟头上有两个洞,伴随着日常清除排放在上部孔。自出生以来就经历了这种抱怨。患者接受了背侧尿道切除术以纠正阴茎异常。
    Urethral duplication is a rare disease with diverse clinical symptoms and more common in male; only fewer than 300 instances have been reported. In this case report, a 20-year-old male patient came to the urology polyclinic with two holes on the glans penis, accompanied by daily clear discharge in the upper hole. This complaint has been experienced since birth. The patient underwent an excision of the dorsal accessory urethra to correct penile anomalies.
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  • 文章类型: Case Reports
    尿道重复是一种罕见的先天性异常;Y形尿道重复是最罕见的变体,缺乏标准化的治疗计划。我们报告了一名9岁的男性患者,在新生儿年龄期间诊断为尿道Y重复,他于2018年在印度的三级护理教学医院就诊。该患者在生命的第七天因肛门通过尿液而接受了膀胱造口术,此后失去了随访。八岁的时候,结肠造口术后从肛门断开重复尿道的尝试失败。患者通过原位尿道进行性扩张成功治疗,这需要多个阶段,随后尿道与直肠分离。在三年的随访中,患者为大陆且无症状。
    Duplication of urethra is a rare congenital anomaly; a Y-shaped urethral duplication is the rarest variant and lacks a standardised treatment plan. We report a nine-year-old male patient with a Y-duplication of urethra diagnosed during neonatal age who presented to a tertiary care teaching hospital in India in 2018. The patient had undergone a vesicostomy on the seventh day of life for passing urine per anus and was lost to follow-up thereafter. At eight years of age, there was a failed attempt at disconnection of the duplicated urethral tract from the anus after colostomy. The patient was managed successfully by progressive dilatation of the orthotopic urethra, which required multiple stages, followed by separation of the urethra from the rectum. At three-years follow-up the patient was continent and asymptomatic.
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  • 文章类型: Case Reports
    尿道重复是一种罕见的先天性畸形。一个14个月大的孩子,性完整,男性,对完全Y型尿道重复的Lagotto犬进行膀胱镜引导激光烧灼的辅助尿道治疗,一个10瓦二极管激光器550微米的光纤和2.3Fr外径。激光烧灼,每14天重复一次,总共三次,是通过从肛周区域的附件尿道出口插入器械,直到尿道镜可以看到它,在坐骨尿道内.然而,这项技术被证明是非侵入性的,比手术便宜,持续时间短,和安全,不允许异常尿道完全闭合。因此,随后进行了附件尿道的手术切除。据作者所知,这是有关膀胱镜引导的二极管激光烧灼术用于辅助尿道治疗的第一份报告。
    Duplication of the urethra is a rare congenital malformation. A 14-month-old, sexually intact, male, Lagotto dog with complete Y-type urethral duplication was subjected to accessory urethra treatment for cystoscopic guided laser cauterization, with a 10-Watt diode laser with 550-micron fiber and 2.3 Fr outer diameter. The laser cauterization, that was repeated every 14 days for a total of three times, was performed by inserting the instrument from the accessory urethra outlet in the perianal area until it could be seen by the urethroscope, inside the ischial urethra. Nevertheless, this technique that proved to be non-invasive, less expensive than surgery, of short duration, and safe, did not allow the complete closure of the abnormal urethral tract. Therefore, the subsequent surgical removal of the accessory urethra was carried out. To the authors\' knowledge this is the first report on the use of cystoscopic guided diode laser cauterization for accessory urethra treatment.
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  • 文章类型: Case Reports
    尿道重复并不常见,文献报道的病例很少。我们报告了一例病例,其中一名患者自童年以来就从阴茎近端排出,并有最近的感染史。诊断为耻骨前窦,并完全切除窦道。
    Urethral duplication is uncommon with few cases reported in the literature. We report a case in which a patient presented with discharge from proximal part of penis since childhood and recent history of infection. The diagnosis of pre-pubic sinus was made and complete excision of the sinus tract was done.
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  • 文章类型: Case Reports
    泌尿生殖道窦(UGS)和泄殖腔畸形是主要影响女性的疾病谱,导致生殖器和泌尿道不寻常的汇合,有或没有胃肠道的参与。这些异常的成功重建取决于在横截面和其他对比研究的帮助下对异常解剖结构进行准确的术前描绘,例如生殖器图以及膀胱尿道镜检查。我们在此报告一例14岁女性,该女性表现为不规则的周期性血尿,并被诊断为持续性UGS伴尿道重复。经过全面评估,患者通过手术重建成功,在这项研究中描述。持续UGS是一种复杂的发育异常。完整的异常特征需要彻底的评估,如激素评估,内窥镜检查,横截面,和放射学对比研究。手术重建需要个体化,可能需要阴蒂成形术,阴唇成形术,尿道和阴道动员。在精心计划的手术重建中,形态和功能结果令人满意。
    Urogenital sinus (UGS) and cloacal malformations are the spectra of disease affecting mainly females, resulting in an unusual confluence of the genital and urinary tract with or without the involvement of the gastrointestinal tract. Successful reconstruction of these anomalies depends on the accurate preoperative delineation of abnormal anatomy with the help of cross-sectional and other contrast studies like genitourogram along with cystourethroscopy wherever indicated. We hereby report a case of a 14-year-old female who presented with irregular cyclical hematuria and was diagnosed with persistent UGS with urethral duplication. After a thorough evaluation, the patient was successfully managed with surgical reconstruction, described in this study. Persistent UGS is a complex developmental anomaly. Complete characterization of anomaly requires a thorough evaluation such as hormonal assessment, endoscopy, cross-sectional, and radiological contrast study. Surgical reconstruction needs individualization and may need clitoroplasty, labioplasty, and urethral and vaginal mobilization. Morphological and functional outcome is satisfactory in a well-planned surgical reconstruction.
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