淋巴管平滑肌瘤病(LAM)是一种罕见的,生长缓慢的转移性肿瘤,其中平滑肌样细胞浸润肺实质并引起囊性肺损伤。常见的早期症状包括呼吸急促,气胸,和胸痛。淋巴管平滑肌瘤病主要累及肺部,肾脏,和淋巴结。这项研究回顾了淋巴管平滑肌瘤病的特征,以确定该疾病症状患病率的任何可能变化。我们对PubMed和GoogleScholar的淋巴管肌瘤病病例报告进行了文献综述。感兴趣的变量是年龄,性别,症状,生命体征,免疫染色,和放射学发现。数据被转移到Excel电子表格(微软公司,雷德蒙德,WA),意思是,中位数,标准偏差,频率,并使用R版本1.1.456计算比例(RStudio:R.RStudio的集成开发,PBC,波士顿,MA).淋巴管肌瘤病是一种罕见的病例,因此在网上找不到多少文献。这项研究包括33例病例报告,女性占演讲人数的78.78%。平均年龄38岁,SD14.41年。呼吸短促是最常见的症状(60.6%),其次是气胸(57.57%),胸痛(42.42%),咳嗽(24.24%),胸腔积液(1.25%)。
Lymphangioleiomyomatosis (LAM) is a rare, slow-growing metastasizing neoplasm in which smooth muscle-like cells infiltrate the lung parenchyma and cause cystic lung damage. The common early symptoms include shortness of breath, pneumothorax, and chest pain. Lymphangioleiomyomatosis mainly involves the lungs, kidneys, and lymph nodes. This study reviews the characteristics of lymphangioleiomyomatosis to identify any possible changes in the prevalence of symptoms of the disease. We conducted a literature review of case reports on lymphangioleiomyomatosis from PubMed and Google Scholar. Variables of interest were age, gender, symptoms, vitals, immunostaining, and radiological findings. Data were transferred to an Excel spreadsheet (Microsoft Corporation, Redmond, WA), and mean, median, standard deviation, frequencies, and proportions were calculated using R version 1.1.456 (RStudio: Integrated Development for R. RStudio, PBC, Boston, MA). Lymphangioleiomyomatosis is a rare case and so not much of the literature could be found online. Thirty-three case reports were included in this study, and females accounted for 78.78% of the presentations. The average age was 38 years, SD 14.41 years. Shortness of breath was the most frequent symptom (60.6%), followed by pneumothorax (57.57%), chest pain (42.42%), cough (24.24%), and pleural effusion (1.25%).