Pectus carinatum

  • 文章类型: Journal Article
    背景:卡氏胸(PC)主要存在于青少年早期或青春期的生长高峰时期。外貌不佳是寻求外科医生帮助以增强自信心和自尊的主要原因。目前,微创修复是矫正胸壁畸形的有效方法之一。因此,开展青少年PC的MIR临床研究具有重要的现实意义。
    方法:我们在PC组中应用了Abramson程序,或者在PC/PE组中应用了Abramson程序和Nuss程序。我们回顾性回顾了2020年1月至2023年4月在我科接受手术矫正的41例患者的结果。
    结果:所有手术均成功完成,无严重并发症。PC组中位手术时间为80min,PC/PE组为130min。PC组LOS中位数为4天,PC/PE组为5天。PC组压缩深度中位数为32mm,PC/PE组为12mm。术后,有一些并发症。两组9例气胸患者均接受保守治疗。一名患者术后过度矫正。两组均有3例钢丝断裂。一名患者术后再次手术,导致钢丝断裂导致棒材脱位。
    结论:Abramson程序或Abramson程序和Nuss程序在修复PC和PC/PE方面具有良好的短期效果。根据Abramson程序后下平面是否过度压下,应分别选择一个或两个程序。
    BACKGROUND: Pectus carinatum (PC) mainly present at the growth spurt time of the early teenage years or the puberty. Poor outer appearance is a major reason for seeking help for surgeons to increase self-confidence and self-esteem. At present, minimally invasive repair (MIR) is one of effective ways to correct the chest wall deformity. Therefore, there is great practical significance to conduct clinical research on MIR about the adolescent PC.
    METHODS: We applied Abramson procedure in PC group or we applied Abramson procedure and Nuss procedure in PC/PE group. We retrospectively reviewed the results of 41 cases who underwent the surgical correction at our department from January 2020 to April 2023.
    RESULTS: All the procedures were successfully done without severe complications. The median operation Time was 80 min in PC group while was 130 min in PC/PE group. The median LOS were 4 days in PC group while 5 days in PC/PE group. The median compression depth was 32 mm in PC group while 12 mm in PC/PE group. Postoperatively, there are some complications. All Pneumothorax patients being treated conservatively were found in 9 patients in two groups. One patient suffered overcorrection after operation. There were 3 patients suffered steel wires breakage in two groups. One patient reoperation postoperatively for the dislocation of the bar secondary to steel wires breakage.
    CONCLUSIONS: The Abramson procedure or Abramson procedure and Nuss procedure have good short-term results in repair PC and PC/PE. Select one or two procedures should be done individually based on whether the lower plane over depressed after Abramson procedure.
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  • 文章类型: Journal Article
    目的:这项研究旨在比较脊柱姿势,移动性,青少年漏斗胸(PE)的位置感和位置感,Carinatum(PC),健康控制(HC)。
    方法:22与PE,22与PC,21HC纳入研究。脊柱姿势(胸椎后凸,腰椎前凸,骨盆倾斜,胸廓,腰椎,骨盆侧向倾角)和活动性(胸椎,腰椎,髋/骶骨,总的来说,在矢状面和额面)与脊髓小鼠,和脊柱位置感觉(复位误差)的倾斜计进行评估。
    结果:PE和PC的胸椎后凸角度高于HC(p<0.001;p=0.001)。PE和PC矢状面的髋/骶骨活动度低于对照组,分别(p<0.001;p<0.001)。PC的总体矢状脊柱活动度(p:0.007)和额平面的髋/骶骨活动度(p:0.002)低于HC。PE和PC的总体额叶脊柱活动度低于HC(p:0.002;p:0.014)。PE和PC复位误差较高(p<0.001;p:0.014)。
    结论:研究发现,患有PE和PC的青少年脊柱活动能力下降,脊柱排列障碍,脊柱位置感下降。在对胸壁畸形的青少年进行身体检查时,重要的是不要忽视脊柱。在临床实践中,我们建议有胸部畸形的青少年应接受脊柱评估,并接受物理治疗以治疗脊柱疾病。
    OBJECTIVE: The study aimed to compare spinal posture, mobility, and position sense in adolescents with pectus excavatum (PE), pectus carinatum (PC), and healthy control (HC).
    METHODS: 22 with PE, 22 with PC, and 21 HC were included in the study. The spinal posture (thoracic kyphosis, lumbar lordosis, pelvic tilt, thoracic, lumbar, pelvic lateral tilt angles) and mobility (thoracic, lumbar, hip/sacral, and overall, in the sagittal and frontal plane) with the spinal mouse, and spinal position sense (repositing errors) with the inclinometer were assessed.
    RESULTS: The thoracic kyphosis angle of PE and PC was higher than in HC (p < 0.001; p = 0.001). Hip/sacral mobility in the sagittal plane was lower in the PE and PC than control, respectively (p < 0.001; p < 0.001). Overall sagittal spinal mobility (p:0.007) and hip/sacral mobility in the frontal plane (p:0.002) were lower in the PC than in HC. Overall frontal spinal mobility was lower in the PE and PC than in HC (p:0.002; p:0.014). The PE and PC repositing errors were higher (p < 0.001; p:0.014).
    CONCLUSIONS: The study found that adolescents with PE and PC had decreased spinal mobility, spinal alignment disorders, and a decline in spinal position sense. It is important not to overlook the spine during physical examinations of adolescents with chest wall deformities. In clinical practice, we suggest that adolescents with chest deformities should undergo a spine evaluation and be referred for physical therapy to manage spinal disorders.
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  • 文章类型: Journal Article
    我们的目的是研究三明治技术联合Harrison沟治疗Carinatum胸膜的可行性。回顾性分析2015年6月至2022年10月收治的38例胸骨合并Harrison沟患儿的临床资料。所有患者均使用三明治技术进行了手术。分析患者手术情况、术后疗效及家属满意度评分。总的来说,患者的平均手术时间为179.05±36.01分钟,术中失血量为10.03±2.77mL,术后住院时间6.89±0.73天,术后满意度为89.4±4.6分。手术并发症发生率为7.89%。22例患者内固定支架拔除,在支架移除后371.4±6.3天的随访中没有复发。这些结果是令人满意的。使用三明治技术治疗这种情况不会减少手术后胸部的体积,并导致美观的切口,并发症少,术后恢复快.因此,是一种安全有效的方法,值得临床推广应用。
    We aimed to investigate the feasibility of the sandwich technique to treat pectus carinatum combined with Harrison sulcus. We retrospectively analysed the clinical data of 38 paediatric patients with pectus carinatum combined with Harrison sulcus treated from June 2015 to October 2022. All the patients underwent surgery using the sandwich technique. The surgical conditions and postoperative outcomes of the patients and the satisfaction score of family members were analysed. Overall, the patients had a mean duration of surgery of 179.05 ± 36.01 min, intraoperative blood loss of 10.03 ± 2.77 mL, postoperative hospital stay of 6.89 ± 0.73 days, and postoperative satisfaction score of 89.4 ± 4.6. The incidence of surgical complications was 7.89%. The internal fixation stents were removed in 22 patients, and there was no recurrence during a follow-up 371.4 ± 6.3 days post-stent removal. These results were satisfactory. The use of the sandwich technique to treat this condition does not reduce the volume of the thorax after the procedure and results in an aesthetically pleasing incision, less complications, and fast postoperative recovery. Thus, it is a safe and effective method that is worthy of being promoted for clinical application.
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  • 文章类型: Journal Article
    胸肌缺陷是在大约250人中发现的一组先天性疾病,胸骨向脊柱(漏斗)方向凹陷,向前突出(carinatum)或更罕见的是两者的混合(弧形或混合缺陷)。对于大多数患者来说,它是很好的耐受性,但是有些病人在心理上受到影响,生理上或两者兼而有之。由于肋骨和将它们连接到胸骨的软骨的生长,畸形在年轻时变得明显。大多数缺陷是轻微的,耐受性良好,即它们不影响活动,也不造成心理伤害。然而,一些年轻人自尊心降低和抑郁,导致他们退出活动(如游泳,跳舞)和可能“暴露”它们的互动(如过夜,约会,去海滩,穿着时髦的衣服)。这种心理伤害发生在他们身体和社会发展的关键时刻。少数患者的胸骨极度抑郁,阻碍了他们的生理储备,这可能发生在进行剧烈运动(如跑步)时,但也可能限制适度的活动,如步行和爬楼梯。这种影响可能是如此极端,以至于在休息时出现症状或导致主要血管和器官受到威胁生命的压迫。患有生理障碍的患者群体通常也患有低自尊和抑郁。本文总结了目前针对这种情况的不同治疗策略的证据,包括支持性护理,心理支持和非手术技术,包括支撑和真空钟形疗法。我们还考虑手术技术,包括Ravitch手术,Nuss手术(漏斗胸微创修复),胸膜植入物和其他罕见的手术,如PectusUp。对于大多数患者来说,支持性护理就足够了,但是对于少数人来说,可以考虑其他技术的组合。本文还概述了提供此类疗法的最佳实践指南,包括标准化评估,同意治疗,审计,质量保证和长期支持。所有干预措施都有患者的风险和益处,父母和临床医生在决定最合适的课程时需要仔细考虑和讨论。我们希望对“Pectus最佳实践”的证据审查将为这些考虑做出重大贡献,并帮助所有相关人员,从病人到国家政策制定者,提供最好的护理。
    Pectus defects are a group of congenital conditions found in approximately 1 in 250 people, where the sternum is depressed back towards the spine (excavatum), protrudes forwards (carinatum) or more rarely is a mixture of both (arcuatum or mixed defects). For the majority of patients, it is well tolerated, but some patients are affected psychologically, physiologically or both. The deformity becomes apparent at a young age due to the growth of the ribs and the cartilage that links them to the sternum. The majority of defects are mild and are well tolerated, i.e. they do not affect activity and do not cause psychological harm. However, some young people develop lower self-esteem and depression, causing them to withdraw from activities (such as swimming, dancing) and from interactions that might \'expose\' them (such as sleepovers, dating, going to the beach and wearing fashionable clothes). This psychological harm occurs at a crucial time during their physical and social development. A small number of patients have more extreme depression of their sternum that impedes their physiological reserve, which can occur when engaging in strenuous exercise (such as running) but can also limit moderate activity such as walking and climbing stairs. The effects can be so extreme that symptoms occur at rest or cause life-threatening compression of the major blood vessels and organs. The group of patients with physiological impairment usually also suffer from low self-esteem and depression. This paper summarizes the current evidence for the different treatment strategies for this condition, including supportive care, psychological support and non-surgical techniques including bracing and vacuum bell therapy. We also consider surgical techniques including the Ravitch procedure, the Nuss procedure (minimally invasive repair of pectus excavatum), pectus implants and other rare procedures such as Pectus Up. For the majority of patients, supportive care is sufficient, but for a minority, a combination of the other techniques may be considered. This paper also outlines best practice guidance for the delivery of such therapies, including standardized assessment, consent to treatment, audit, quality assurance and long-term support. All the interventions have risks and benefits that the patient, parents and clinicians need to carefully consider and discuss when deciding on the most appropriate course. We hope this evidence review of \'Best Practice for Pectus\' will make a significant contribution to those considerations and help all involved, from patients to national policy makers, to deliver the best possible care.
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  • 文章类型: Journal Article
    本文回顾了漏斗胸,Carinatum,和弧形。涵盖的主题包括病因,流行病学,相关综合征,生理影响,workup,治疗适应症,手术和非手术治疗,结果,并发症,和新兴疗法。漏斗胸是胸骨和/或前胸壁的向内变形。胸骨是一种胸骨的向外突出或倾斜,具有潜在的心理影响,但没有表现出生理影响。在符合支撑程序的胸壁柔韧性患者中,非手术压迫支撑是成功的。胸骨是一个异常短,胸骨完全融合,前突高。
    This article reviews pectus excavatum, carinatum, and arcuatum. Topics covered include etiology, epidemiology, associated syndromes, physiologic impact, workup, indications for treatment, surgical and nonsurgical therapy, results, complications, and emerging therapies. Pectus excavatum is an inward deformation of the sternum and/or anterior chest wall. Pectus carinatum is ether an outward protrusion or tilt of the sternum with potential psychological impact, but no demonstrated physiologic impact. Nonoperative compression bracing is successful in carinatum patients with chest wall flexibility who are compliant with a bracing program. Pectus arcuatum is an abnormally short, fully fused sternum with a high anterior protrusion.
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  • 文章类型: Journal Article
    目的:探讨不同类型的前胸壁与脊柱畸形的关系及特点。
    方法:共纳入548例前胸壁畸形患者。进行临床和放射学检查以确定脊柱畸形。评估脊柱畸形的类型和严重程度,并对其与胸壁畸形亚型的关系进行统计学分析。
    结果:在93例(16.97%)患者中发现脊柱畸形。患者分为71例(76.3%)男性和22例(23.7%)女性患者。在418例漏斗胸(PE)患者中,有57例(13%)发现了脊柱畸形,在117例胸膜(PC)患者中,有23例(19%),在所有混合性胸膜畸形(PE+PC)患者中,综合征畸形和肋骨异常。在PE组,脊柱侧弯,后凸畸形分别为57.9%和31.6%,分别。在PC组中,这些比率分别为43.5和47.8%,分别。特发性脊柱侧凸有42例(77.7%),是最常见的脊柱侧凸亚组。主要的胸廓弯曲是最常见的曲线,在15例(35.7%)特发性脊柱侧凸患者中观察到。
    结论:特发性脊柱侧凸以主胸曲为最常见的前胸壁畸形。脊柱畸形在男性胸部畸形患者中更为常见。在大量的PE和PC患者中发现脊柱后凸。PE和PC混合的患者,肋骨异常,和综合征性疾病更可能有脊柱畸形。
    OBJECTIVE: To investigate the association and evaluate the characteristics between different types of anterior chest wall and spinal deformities.
    METHODS: A total of 548 patients with anterior chest wall deformities were included in this study. Clinical and radiological examinations were performed to determine spinal deformities. The type and severity of the spinal deformities were evaluated and their relationships with chest wall deformity subtypes were statistically analyzed.
    RESULTS: Spinal deformities were identified in 93 (16.97%) patients. The patients were subdivided into 71 (76.3%) male and 22 (23.7%) female patients. A spinal deformity was detected in 57 (13%) of 418 pectus excavatum (PE) patients, in 23 (19%) of 117 pectus carinatum (PC) patients, and in all patients with mixed pectus deformity (PE + PC), syndromic deformity and rib anomalies. In the PE group, scoliosis, and kyphosis were observed at 57.9 and 31.6%, respectively. In the PC group, these rates were 43.5 and 47.8%, respectively. Idiopathic scoliosis was observed in 42 (77.7%) and constituted the most common scoliosis subgroup. The main thoracic curvature was the most common curve pattern, which was observed in 15 (35.7%) patients with idiopathic scoliosis.
    CONCLUSIONS: Idiopathic scoliosis with main thoracic curvature is the most common deformity in patients with anterior chest wall deformity. Spinal deformities are more common in male patients with chest deformities. Kyphosis is found in a significant number of PE and PC patients. Patients with mixed PE and PC, rib anomalies, and syndromic disease are more likely to have spinal deformities.
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  • 文章类型: Case Reports
    背景:已经使用Abramson技术进行了隆胸(MIRPC)的微创修复,其中压缩胸骨的棒用钢丝固定在肋骨上。一名14岁的患者使用夹层技术接受了MIRPC治疗,其中在胸腔镜视野下将两个固定有桥的金属棒植入胸骨下方,皮下隧道中的另一个酒吧被植入上面。这种技术有可能避免与原始技术相关的特定问题,如松动矫正支持(断线),避免诱发漏斗胸或皮下组织粘连。
    BACKGROUND: Minimally invasive repair of pectus carinatum (MIRPC) has been performed using the Abramson technique in which the bar that compresses the sternum is fixed with steel wires on the ribs. A 14-year-old patient underwent to a MIRPC using a sandwich technique in which two metallic bars fixed with bridges were implanted below the sternum under thoracoscopic vision, and another bar in a subcutaneous tunnel was implanted above. This technique has the potential to avoid specific problems related to the original technique like loosening of support for correction (broken wire), avoidance of induction of pectus excavatum or subcutaneous tissue adhesion.
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  • 文章类型: Journal Article
    背景:胸骨,也被称为转向角异常或Currarino-Silverman综合征,是一种明显的胸骨异常,以严重的胸骨角化为特征,一个缩短的胸骨,和轻度漏斗胸.异常通常使用开放式技术修复,采用矫形固定装置。这里,我们报告了微创混合手术修复弓形胸肌的结果。
    方法:该手术结合了标准的Nuss手术,以矫正胸骨凹陷与上胸部短切口(男孩)或乳房间切口(女孩),用于双侧软骨下切除上肋软骨,截骨,以及手动角度的校正。回顾了过去10年中接受该手术的所有患者的医疗记录。
    结果:5名患者,3个男孩和2个女孩,14至17岁,接受了程序。修复后3-4年,三名患者的胸肌条被移除。矫正后随访6个月至7年。良好的矫正使所有患者恢复,无并发症和复发。迄今为止,所有患者都对他们的结果感到满意。
    结论:微创混合手术充分矫正了弓形胸骨,疤痕最小,满意度高。
    BACKGROUND: Pectus arcuatum, also known as horns of steer anomaly or Currarino-Silverman Syndrome, is a distinct chest wall anomaly characterized by severe manubriosternal angulation, a shortened sternum, and mild pectus excavatum. The anomaly is typically repaired using open techniques, employing orthopedic fixation devices. Here, we report the results of a minimally invasive hybrid procedure to repair pectus arcuatum.
    METHODS: The procedure combines a standard Nuss procedure to correct the depressed sternum with a short upper chest (in boys) or inter-mammary (in girls) incision for bilateral subperichondrial resection of the upper costal cartilages, osteotomy, and correction of the manubrial angulation. The medical records of all patients who underwent the procedure over the last 10 years were reviewed.
    RESULTS: Five patients, 3 boys and 2 girls, aged 14 to 17 years, underwent the procedure. Three patients had their pectus bars removed 3-4 years after repair. Follow-up after correction ranged from 6 months to 7 years. Good correction resulted in all patients achieving recovery without complications and recurrence. To date, all patients have been satisfied with their results.
    CONCLUSIONS: The minimally invasive hybrid procedure adequately corrects pectus arcuatum with minimal scarring and high satisfaction.
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  • 文章类型: Journal Article
    背景:虽然有效,Carinatum儿童的压缩矫形支撑(COB)仍未标准化。本研究旨在分析胸墙国际集团(CWIG)成员的当前做法。
    方法:向208个部门的所有CWIG成员邮寄了一份基于网络的问卷。它包括30个关于诊断工作的问题,COB适应症的年龄,使用的COB类型,每日佩戴时间,治疗持续时间,并发症,和复发率。
    结果:来自44个部门的成员做出了回应(机构回应率为21.2%)。93%的人认为COB是PC的一线治疗。传统COB(CC)的使用率为59%,而动态压缩系统(FMF)占41%。总体符合率>80%。总共67%的应答者认为COB适用于<10年的患者。实际佩戴时间明显短于医师推荐的时间(p<0.01)。FMF患者的反应明显快于CC患者(p<0.01)。在34%中没有发现PC复发;在61%中发现10-30%的复发率。
    结论:COB是PC的一线治疗方法,依从率高。在青春期,复发率高。建议将治疗标准化并随访至青春期结束,以提高COB的有效性。
    BACKGROUND: Although effective, compressive orthotic bracing (COB) in children with pectus carinatum is still not standardized. This study has aimed to analyze current practices amongst members of the Chest Wall International Group (CWIG).
    METHODS: A web-based questionnaire was mailed to all CWIG members at 208 departments. It included 30 questions regarding diagnostic work-up, age for COB indication, type of COB used, daily wearing time, treatment duration, complications, and recurrence rate.
    RESULTS: Members from 44 departments have responded (institutional response rate 21.2%). A total of 93% consider COB as the first-line treatment for PC. A conventional COB (CC) is used in 59%, and the dynamic compression system (FMF) in 41%. The overall compliance rate is >80%. A total of 67% of responders consider COB to be indicated in patients <10 years. The actual wearing time is significantly shorter than the physician-recommended time (p < 0.01). FMF patients experience a significantly faster response than CC patients (p < 0.01). No recurrence of PC has been noted in 34%; recurrence rates of 10-30% have been noted in 61%.
    CONCLUSIONS: COB is the first-line treatment for PC with a high compliance rate. During puberty, the recurrence rate is high. Treatment standardization and follow-up until the end of puberty are recommended to enhance COB effectiveness.
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  • 文章类型: Journal Article
    目的:本研究旨在回顾性评估对新开发的压缩支具的反应,以改善接受中线胸骨切开术心脏手术的婴幼儿继发性胸肌畸形。确定了影响对支具反应的因素。
    方法:纳入51名儿童。严重程度表示为从胸部X射线获得的胸骨的突出角度。根据开始时的角度与其佩戴支具后的百分比变化之间的关系的正或负二元残差,将患者分为两组。采用Logistic回归分析确定影响因素。
    结果:30名患者(58.8%)显示该关系的零和正残差(良好的反应者,G组),而21例患者显示阴性残差(反应不良,P组)。男性,严重心脏异常,复杂的外科手术,多发性胸骨切开术,总持续时间,通过单因素分析,自我停药与对支具的反应不良相关。通过多变量分析,前三个因素仍然具有高的响应差的优势比。支具未发生不良事件。
    结论:我们新开发的压缩支撑做出了贡献,至少在某种程度上,改善次生隆胸畸形。需要进一步的研究来阐明前胸按压对继发性胸骨的治疗效果。
    OBJECTIVE: This study aimed to retrospectively assess the response to a newly developed compression brace for improving the deformity of the secondary pectus carinatum in infants and toddlers undergoing cardiac surgery with midline sternotomy. Factors affecting the response to the brace were identified.
    METHODS: Fifty-one children were enrolled. Severity was expressed as the protrusion angle of the sternum obtained from chest X-ray. The patients were divided into two groups by positive or negative binary residuals of the relationship between the angle at the beginning and its percentage change after wearing the brace. Logistic regression analysis was used to identify the influencing factors.
    RESULTS: Thirty patients (58.8%) showed zero and positive residuals to the relationship (good responders, Group G), whereas 21 patients showed negative residuals (poor responders, Group P). Male sex, severe cardiac anomaly, complex surgical procedure, multiple sternotomy, total duration, and self-discontinuation were associated with poor response to the brace by univariate analysis. The first three factors remained with high odds ratio for poor response by multivariate analysis. No adverse events occurred with the brace.
    CONCLUSIONS: Our newly developed compression brace contributed, at least in part, to improve the deformity of the secondary pectus carinatum. Further studies are required to clarify the therapeutic efficacy of anterior chest compression for secondary pectus carinatum.
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